Bibliographic Details
| Title: |
Evaluation of global and regional myocardial work by echocardiography in patients with Fabry disease |
| Authors: |
Han Wang, Ying Yang, Lin Liu, Yawen Zhao, Yang Li, Wei Zhang, Wei Ma |
| Source: |
Orphanet Journal of Rare Diseases, Vol 19, Iss 1, Pp 1-9 (2024) |
| Publisher Information: |
BMC, 2024. |
| Publication Year: |
2024 |
| Collection: |
LCC:Medicine |
| Subject Terms: |
Medicine |
| More Details: |
Abstract Background This study aimed to quantitatively evaluate the left ventricular global and regional myocardial work of patients in Fabry disease (FD) by echocardiographic pressure–strain loop (PSL) analysis. Results The study included 48 patients with FD and 48 healthy controls matched for age and sex. According to the presence/absence of left ventricular hypertrophy (LVH), the patients with FD were divided into an LVH + group and an LVH– group. Left ventricular blood pressure was estimated noninvasively according to echocardiographic valvular events and systolic pressure in the brachial artery. Left ventricular myocardial work parameters were acquired by echocardiographic pressure–strain loop analysis. The FD groups had a significantly lower global longitudinal strain (GLS), global work index, global work efficiency (GWE), global constructive work and higher global waste work than the control group (P |
| Document Type: |
article |
| File Description: |
electronic resource |
| Language: |
English |
| ISSN: |
1750-1172 |
| Relation: |
https://doaj.org/toc/1750-1172 |
| DOI: |
10.1186/s13023-024-03396-3 |
| Access URL: |
https://doaj.org/article/881d0dcfeb26452ba9404689de5ff226 |
| Accession Number: |
edsdoj.881d0dcfeb26452ba9404689de5ff226 |
| Database: |
Directory of Open Access Journals |
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