Case Report: Life-Threatening Post-operative Hemorrhage in Klippel–Trenaunay Syndrome Associated With Hypofibrinogenemia

Bibliographic Details
Title: Case Report: Life-Threatening Post-operative Hemorrhage in Klippel–Trenaunay Syndrome Associated With Hypofibrinogenemia
Authors: Hongna Yang, Binfeng Du, Han Liu, Yong Yao, Chen Li
Source: Frontiers in Medicine, Vol 8 (2021)
Publisher Information: Frontiers Media S.A., 2021.
Publication Year: 2021
Collection: LCC:Medicine (General)
Subject Terms: conservative therapy, fibrinogen concentrate, hypofibrinogenemia, klipple-trenaunay syndrome, post-operative hemorrhage, prophylactic transfusion of fibrinogen, Medicine (General), R5-920
More Details: Klippel–Trenaunay Syndrome (KTS) is a rare congenital disorder, characterized by venous and lymphatic malformations of the skin, soft tissue, and bone, causing limb hypertrophy. Although, a ruptured hemorrhagic corpus luteum is a rare condition in women of reproductive age, it can result in lethal outcomes. Here, we have described a patient with KTS and hypofibrinogenemia who went through recurrent lethal postoperative bleeding due to a ruptured hemorrhagic corpus luteum. This case suggested that conservative therapy might be the first choice and effective therapy for the patients with KTS, who suffered from bleeding complications of surgical therapy.
Document Type: article
File Description: electronic resource
Language: English
ISSN: 2296-858X
Relation: https://www.frontiersin.org/articles/10.3389/fmed.2021.669793/full; https://doaj.org/toc/2296-858X
DOI: 10.3389/fmed.2021.669793
Access URL: https://doaj.org/article/52ab6c1e700249afb37e5039d0a9dbf4
Accession Number: edsdoj.52ab6c1e700249afb37e5039d0a9dbf4
Database: Directory of Open Access Journals
More Details
ISSN:2296858X
DOI:10.3389/fmed.2021.669793
Published in:Frontiers in Medicine
Language:English