Bibliographic Details
Title: |
Intravenous immunoglobulin treatment stabilizing a patient with Anti-PL7 antisynthetase syndrome with interstitial lung disease and eosinophilic inflammation |
Authors: |
Soran Peshbahar, Charlotte Hyldgaard, Elisabeth Bendstrup |
Source: |
Respiratory Medicine Case Reports, Vol 38, Iss , Pp 101686- (2022) |
Publisher Information: |
Elsevier, 2022. |
Publication Year: |
2022 |
Collection: |
LCC:Diseases of the respiratory system |
Subject Terms: |
Antisynthetase syndrome (AS), Interstitial lung disease (ILD), Intravenous immunoglobulin (IVIG), Anti-PL7, Eosinophilic inflammation, Diseases of the respiratory system, RC705-779 |
More Details: |
Antisynthetase syndrome (AS) is a rare autoimmune disease characterized by autoantibodies against aminoacyl-transfer RNA synthetase and clinical features which can include interstitial lung disease (ILD). Current available evidence of treatment is based on expert opinions and case reports. Here, we present a patient with an initial diagnosis of eosinophilic pneumonia, who was later diagnosed with anti-PL7 antisynthetase syndrome with ILD and eosinophilic inflammation. The patient was non-responsive to classic immunosuppressants but responded remarkably well to intravenous immunoglobulin. |
Document Type: |
article |
File Description: |
electronic resource |
Language: |
English |
ISSN: |
2213-0071 |
Relation: |
http://www.sciencedirect.com/science/article/pii/S2213007122001083; https://doaj.org/toc/2213-0071 |
DOI: |
10.1016/j.rmcr.2022.101686 |
Access URL: |
https://doaj.org/article/4cfb434d48ee4097a7a2b26445528cc8 |
Accession Number: |
edsdoj.4cfb434d48ee4097a7a2b26445528cc8 |
Database: |
Directory of Open Access Journals |