What's behind your eosinophilic myocarditis? A case of Churg–Strauss syndrome diagnosed during acute heart failure

Bibliographic Details
Title: What's behind your eosinophilic myocarditis? A case of Churg–Strauss syndrome diagnosed during acute heart failure
Authors: Nicola Amelotti, Massimo Mapelli, Marco Guglielmo, Maria Inês Fiuza Branco Pires, Jeness Campodonico, Benedetta Majocchi, Valentina Ribatti, Giulia Vettor, Andrea Baggiano, Valentina Catto, Cristina Basso, Gianluca Pontone, Piergiuseppe Agostoni
Source: ESC Heart Failure, Vol 10, Iss 1, Pp 709-715 (2023)
Publisher Information: Wiley, 2023.
Publication Year: 2023
Collection: LCC:Diseases of the circulatory (Cardiovascular) system
Subject Terms: Eosinophilic granulomatosis with polyangiitis (Churg–Strauss), Eosinophilic myocarditis, Heart failure, Endomyocardial biopsy, Cardiac magnetic resonance, Diseases of the circulatory (Cardiovascular) system, RC666-701
More Details: Abstract Eosinophilic granulomatosis with polyangiitis (EGPA) is a rare multisystem disorder; cardiac involvement may include eosinophilic myocarditis. A 67‐year‐old woman presented with 1‐week history of dyspnoea and orthopnoea. She had a history of adult‐onset asthma and peripheral eosinophilia. The investigations showed T‐wave inversion on lateral leads, peripheral eosinophilia, elevated troponin and BNP values, and severe biventricular systolic dysfunction with diffuse hypokinesia and apical akinesia. Computed tomography excluded coronary disease and showed bilateral basal ground‐glass opacities, air‐space consolidation, and bilateral reticular‐nodular pattern. Cardiac magnetic resonance findings were compatible with active myocardial inflammation. An endomyocardial biopsy (EMB) confirmed the diagnosis of eosinophilic myocarditis, and a therapy with oral corticosteroids and heart failure medications was started.
Document Type: article
File Description: electronic resource
Language: English
ISSN: 2055-5822
Relation: https://doaj.org/toc/2055-5822
DOI: 10.1002/ehf2.14172
Access URL: https://doaj.org/article/4b4fc40de8fc4e5ba08f3689c506705f
Accession Number: edsdoj.4b4fc40de8fc4e5ba08f3689c506705f
Database: Directory of Open Access Journals
More Details
ISSN:20555822
DOI:10.1002/ehf2.14172
Published in:ESC Heart Failure
Language:English