Lipofibromatosis: A Rare Diagnosis on Fine Needle Aspiration Cytology

Bibliographic Details
Title: Lipofibromatosis: A Rare Diagnosis on Fine Needle Aspiration Cytology
Authors: Arti KHATRI, Nidhi MAHAJAN, Mamta SENGAR, Anil AGARWAL
Source: Türk Patoloji Dergisi, Vol 36, Iss 3, Pp 268-274 (2020)
Publisher Information: Federation of Turkish Pathology Societies, 2020.
Publication Year: 2020
Collection: LCC:Pathology
Subject Terms: lipofibromatosis, cytology, pediatric, recurrence, Pathology, RB1-214
More Details: Lipofibromatosis is a recently recognized slow growing rare pediatric tumor. Paucity of its cytological description in the literature leads to its pre operative misdiagnosis and further incomplete management. A twelve-month-old female presented with a rapidly progressive mass in the right thigh and buttock region. On examination, the mass was huge and involved the medial, posterior and lateral aspects of the thigh. The cytological smears showed mature adipocytes with few spindled out cells. FNA was reported as a lipoma, corroborating with the radiological presumptive diagnosis. However, histopathological and immunohistochemical features favoured a diagnosis of Lipofibromatosis. The cytological smears were reviewed and a cyto-histo correlation was established. The diagnosis of Lipofibromatosis rests upon classical cytological features in a clinically and radiologically suggestive picture. An early and accurate diagnosis if established can help the surgeon plan excision with wider margins as incomplete excision is associated with a high rate of recurrence.
Document Type: article
File Description: electronic resource
Language: English
ISSN: 1018-5615
1309-5730
Relation: http://www.turkjpath.org/pdf.php3?id=1916; https://doaj.org/toc/1018-5615; https://doaj.org/toc/1309-5730
DOI: 10.5146/tjpath.2020.01479
Access URL: https://doaj.org/article/4af44f3cc70e449085665bbbea55db05
Accession Number: edsdoj.4af44f3cc70e449085665bbbea55db05
Database: Directory of Open Access Journals
More Details
ISSN:10185615
13095730
DOI:10.5146/tjpath.2020.01479
Published in:Türk Patoloji Dergisi
Language:English