Bibliographic Details
| Title: |
Alien-hand syndrome with mirror movements in hereditary diffuse leukoencephalopathy with spheroids. |
| Authors: |
Dongre, Nikhil1, Ambwani, Varsha1, Mani, Vinita Elizabeth1, Paliwal, Vimal Kumar1 dr_vimalkpaliwal@rediffmail.com |
| Source: |
Practical Neurology. Aug2022, Vol. 22 Issue 4, p1-4. 4p. |
| Subject Terms: |
*BRAIN diseases, *ALIEN hand syndrome, *MOVEMENT disorders, *MAGNETIC resonance imaging, *HAND, *PARKINSON'S disease, *DEMENTIA, *STEM cells |
| Abstract: |
Hereditary diffuse leukoencephalopathy with spheroids is a rare genetic disorder caused by mutations of the colony-stimulating factor 1 receptor gene. It is an adult-onset leukodystrophy, with a wide spectrum of neurological and psychiatric manifestations that includes Parkinsonism, dementia, seizures, limb weakness, spasticity and abnormal motor behaviour. Alien-hand syndrome and mirror movements are rare manifestations of this and other neurodegenerative disorders. We describe a woman with progressive limb and trunk rigidity, Parkinsonism and dementia, who also had involuntary left arm levitation (part of the posterior variant of alien-hand syndrome) and left-hand mirror movements. We discuss the different types of alien-hand syndrome, and the likely mechanisms of arm levitation and mirror movements. [ABSTRACT FROM AUTHOR] |
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| Database: |
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