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Vasculitis and vasculopathy associated with inborn errors of immunity: an overview

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Title: Vasculitis and vasculopathy associated with inborn errors of immunity: an overview
Authors: Silvia Federici, Bianca Laura Cinicola, Francesco La Torre, Riccardo Castagnoli, Vassilios Lougaris, Giuliana Giardino, Stefano Volpi, Roberta Caorsi, Lucia Leonardi, Stefania Corrente, Annarosa Soresina, Caterina Cancrini, Antonella Insalaco, Marco Gattorno, Fabrizio De Benedetti, Gian Luigi Marseglia, Michele Miraglia Del Giudice, Fabio Cardinale
Source: Frontiers in Pediatrics, Vol 11 (2024)
Publisher Information: Frontiers Media S.A., 2024.
Publication Year: 2024
Collection: LCC:Pediatrics
Subject Terms: autoinflammatory diseases, DADA2, SAVI, monogenic lupus, haploinsufficiency A20, vasculopathy, Pediatrics, RJ1-570
More Details: Systemic autoinflammatory diseases (SAIDs) are disorders of innate immunity, which are characterized by unprovoked recurrent flares of systemic inflammation often characterized by fever associated with clinical manifestations mainly involving the musculoskeletal, mucocutaneous, gastrointestinal, and nervous systems. Several conditions also present with varied, sometimes prominent, involvement of the vascular system, with features of vasculitis characterized by variable target vessel involvement and organ damage. Here, we report a systematic review of vasculitis and vasculopathy associated with inborn errors of immunity.
Document Type: article
File Description: electronic resource
Language: English
ISSN: 2296-2360
Relation: https://www.frontiersin.org/articles/10.3389/fped.2023.1258301/full; https://doaj.org/toc/2296-2360
DOI: 10.3389/fped.2023.1258301
Access URL: https://doaj.org/article/72787061944f423ca9c03056564a8f03
Accession Number: edsdoj.72787061944f423ca9c03056564a8f03
Database: Directory of Open Access Journals
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  Data: Vasculitis and vasculopathy associated with inborn errors of immunity: an overview
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  Data: <searchLink fieldCode="AR" term="%22Silvia+Federici%22">Silvia Federici</searchLink><br /><searchLink fieldCode="AR" term="%22Bianca+Laura+Cinicola%22">Bianca Laura Cinicola</searchLink><br /><searchLink fieldCode="AR" term="%22Francesco+La+Torre%22">Francesco La Torre</searchLink><br /><searchLink fieldCode="AR" term="%22Riccardo+Castagnoli%22">Riccardo Castagnoli</searchLink><br /><searchLink fieldCode="AR" term="%22Vassilios+Lougaris%22">Vassilios Lougaris</searchLink><br /><searchLink fieldCode="AR" term="%22Giuliana+Giardino%22">Giuliana Giardino</searchLink><br /><searchLink fieldCode="AR" term="%22Stefano+Volpi%22">Stefano Volpi</searchLink><br /><searchLink fieldCode="AR" term="%22Roberta+Caorsi%22">Roberta Caorsi</searchLink><br /><searchLink fieldCode="AR" term="%22Lucia+Leonardi%22">Lucia Leonardi</searchLink><br /><searchLink fieldCode="AR" term="%22Stefania+Corrente%22">Stefania Corrente</searchLink><br /><searchLink fieldCode="AR" term="%22Annarosa+Soresina%22">Annarosa Soresina</searchLink><br /><searchLink fieldCode="AR" term="%22Caterina+Cancrini%22">Caterina Cancrini</searchLink><br /><searchLink fieldCode="AR" term="%22Antonella+Insalaco%22">Antonella Insalaco</searchLink><br /><searchLink fieldCode="AR" term="%22Marco+Gattorno%22">Marco Gattorno</searchLink><br /><searchLink fieldCode="AR" term="%22Fabrizio+De+Benedetti%22">Fabrizio De Benedetti</searchLink><br /><searchLink fieldCode="AR" term="%22Gian+Luigi+Marseglia%22">Gian Luigi Marseglia</searchLink><br /><searchLink fieldCode="AR" term="%22Michele+Miraglia+Del+Giudice%22">Michele Miraglia Del Giudice</searchLink><br /><searchLink fieldCode="AR" term="%22Fabio+Cardinale%22">Fabio Cardinale</searchLink>
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  Data: Frontiers in Pediatrics, Vol 11 (2024)
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  Data: <searchLink fieldCode="DE" term="%22autoinflammatory+diseases%22">autoinflammatory diseases</searchLink><br /><searchLink fieldCode="DE" term="%22DADA2%22">DADA2</searchLink><br /><searchLink fieldCode="DE" term="%22SAVI%22">SAVI</searchLink><br /><searchLink fieldCode="DE" term="%22monogenic+lupus%22">monogenic lupus</searchLink><br /><searchLink fieldCode="DE" term="%22haploinsufficiency+A20%22">haploinsufficiency A20</searchLink><br /><searchLink fieldCode="DE" term="%22vasculopathy%22">vasculopathy</searchLink><br /><searchLink fieldCode="DE" term="%22Pediatrics%22">Pediatrics</searchLink><br /><searchLink fieldCode="DE" term="%22RJ1-570%22">RJ1-570</searchLink>
– Name: Abstract
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  Data: Systemic autoinflammatory diseases (SAIDs) are disorders of innate immunity, which are characterized by unprovoked recurrent flares of systemic inflammation often characterized by fever associated with clinical manifestations mainly involving the musculoskeletal, mucocutaneous, gastrointestinal, and nervous systems. Several conditions also present with varied, sometimes prominent, involvement of the vascular system, with features of vasculitis characterized by variable target vessel involvement and organ damage. Here, we report a systematic review of vasculitis and vasculopathy associated with inborn errors of immunity.
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  Data: 2296-2360
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  Data: https://www.frontiersin.org/articles/10.3389/fped.2023.1258301/full; https://doaj.org/toc/2296-2360
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