Increased RhoA pathway activation downstream of αIIbβ3/SRC contributes to heterozygous Bernard Soulier syndrome

Authors: Larissa Lordier, Christian A. Di Buduo, Alexandre Kauskot, Nathalie Balayn, Cécile Lavenu-Bombled, Francesco Baschieri, Valérie Proulle, Cecilia P. Marin Oyarzun, Francesca Careddu, Ida Biunno, Tudor Manoliu, Philippe Rameau, Isabelle Plo, Nicolas Papadopoulos, Stefan Constantinescu, William Vainchenker, Guillaume Nam Nguyen, Paola Ballerini, Remi Favier, Alessandra Balduini, Hana Raslova

Source: Haematologica, Vol 999, Iss 1 (2025)

Subject Terms: Diseases of the blood and blood-forming organs, RC633-647.5

File Description: electronic resource

Relation: https://haematologica.org/article/view/11965; https://doaj.org/toc/0390-6078; https://doaj.org/toc/1592-8721

Access URL: https://doaj.org/article/ba9a3090e0964f49a274ffcc5b89c862

The IgG-degrading enzyme, Imlifidase, restores the therapeutic activity of FVIII in inhibitor-positive hemophilia A mice

Authors: Melissa Bou-Jaoudeh, Sandrine Delignat, Victoria Daventure, Jan Astermark, Hervé Lévesque, Jordan D. Dimitrov, Claire Deligne, Valérie Proulle, Sébastien Lacroix-Desmazes

Source: Haematologica, Vol 108, Iss 5 (2023)

Subject Terms: Diseases of the blood and blood-forming organs, RC633-647.5

File Description: electronic resource

Relation: https://haematologica.org/article/view/10938; https://doaj.org/toc/0390-6078; https://doaj.org/toc/1592-8721

Access URL: https://doaj.org/article/9ef633a3841246aeb61a09081db47918

A Diagnostic Solution for Lupus Anticoagulant Testing in Patients Taking Direct Oral FXa Inhibitors Using DOAC Filter

Authors: Carine Farkh, Syrine Ellouze, Louis Gounelle, Mama Sad Houari, Jérôme Duchemin, Valérie Proulle, Michaela Fontenay, Xavier Delavenne, Georges Jourdi

Source: Frontiers in Medicine, Vol 8 (2021)

Subject Terms: rivaroxaban, lupus anticoaglant, antiphospholipid antibodies, direct oral anitcoagulant, apixaban, Medicine (General), R5-920

File Description: electronic resource

Relation: https://www.frontiersin.org/articles/10.3389/fmed.2021.683357/full; https://doaj.org/toc/2296-858X

Access URL: https://doaj.org/article/b68bcf452eed45ec8d79b4da41113d27

Rapid Gardos Hereditary Xerocytosis Diagnosis in 8 Families Using Reticulocyte Indices

Authors: Véronique Picard, Corinne Guitton, Lamisse Mansour-Hendili, Bernard Jondeau, Laurence Bendélac, Maha Denguir, Julien Demagny, Valérie Proulle, Frédéric Galactéros, Loic Garçon

Source: Frontiers in Physiology, Vol 11 (2021)

Subject Terms: reticulocytes, Piezo1, xerocytosis, Gardos, red cell indices, Physiology, QP1-981

File Description: electronic resource

Relation: https://www.frontiersin.org/articles/10.3389/fphys.2020.602109/full; https://doaj.org/toc/1664-042X

Access URL: https://doaj.org/article/31491852c95e4e7a8d8a25a25a90446b

Relevance of platelet desialylation and thrombocytopenia in type 2B von Willebrand disease: preclinical and clinical evidence

Authors: Annabelle Dupont, Christelle Soukaseum, Mathilde Cheptou, Frédéric Adam, Thomas Nipoti, Marc-Damien Lourenco-Rodrigues, Paulette Legendre, Valérie Proulle, Antoine Rauch, Charlotte Kawecki, Marijke Bryckaert, Jean-Philippe Rosa, Camille Paris, Catherine Ternisien, Pierre Boisseau, Jenny Goudemand, Delphine Borgel, Dominique Lasne, Pascal Maurice, Peter J. Lenting, Cécile V. Denis, Sophie Susen, Alexandre Kauskot

Source: Haematologica, Vol 104, Iss 12 (2019)

Subject Terms: Diseases of the blood and blood-forming organs, RC633-647.5

File Description: electronic resource

Relation: https://haematologica.org/article/view/9172; https://doaj.org/toc/0390-6078; https://doaj.org/toc/1592-8721

Access URL: https://doaj.org/article/c6a2a981946540fc902c3cbea7dc27d8

Clinical and biological features in PIEZO1-hereditary xerocytosis and Gardos channelopathy: a retrospective series of 126 patients

Authors: Véronique Picard, Corinne Guitton, Isabelle Thuret, Christian Rose, Laurence Bendelac, Kaldoun Ghazal, Patricia Aguilar-Martinez, Catherine Badens, Claire Barro, Claire Bénéteau, Claire Berger, Pascal Cathébras, Eric Deconinck, Jacques Delaunay, Jean-Marc Durand, Nadia Firah, Frédéric Galactéros, Bertrand Godeau, Xavier Jaïs, Jean-Pierre de Jaureguiberry, Camille Le Stradic, François Lifermann, Robert Maffre, Gilles Morin, Julien Perrin, Valérie Proulle, Marc Ruivard, Fabienne Toutain, Agnès Lahary, Loïc Garçon

Source: Haematologica, Vol 104, Iss 8 (2019)

Subject Terms: Diseases of the blood and blood-forming organs, RC633-647.5

File Description: electronic resource

Relation: https://haematologica.org/article/view/9003; https://doaj.org/toc/0390-6078; https://doaj.org/toc/1592-8721

Access URL: https://doaj.org/article/9ac46b6e28d84c27925f98425e20b6c3

Macrophage scavenger receptor SR-AI contributes to the clearance of von Willebrand factor

Authors: Nikolett Wohner, Vincent Muczynski, Amel Mohamadi, Paulette Legendre, Valérie Proulle, Gabriel Aymé, Olivier D. Christophe, Peter J. Lenting, Cécile V. Denis, Caterina Casari

Source: Haematologica, Vol 103, Iss 4 (2018)

Subject Terms: Diseases of the blood and blood-forming organs, RC633-647.5

File Description: electronic resource

Relation: https://haematologica.org/article/view/8426; https://doaj.org/toc/0390-6078; https://doaj.org/toc/1592-8721

Access URL: https://doaj.org/article/262372d980554845a2e76f26c83ee609

Red blood cell Gardos channel (KCNN4): the essential determinant of erythrocyte dehydration in hereditary xerocytosis

Authors: Raphaël Rapetti-Mauss, Véronique Picard, Corinne Guitton, Khaldoun Ghazal, Valérie Proulle, Catherine Badens, Olivier Soriani, Loïc Garçon, Hélène Guizouarn

Source: Haematologica, Vol 102, Iss 10 (2017)

Subject Terms: Diseases of the blood and blood-forming organs, RC633-647.5

File Description: electronic resource

Relation: https://haematologica.org/article/view/8239; https://doaj.org/toc/0390-6078; https://doaj.org/toc/1592-8721

Access URL: https://doaj.org/article/2ee5ded7fbf34d9fa90f899b9717f24b

Risk Factors for Thrombosis in an African Population

Authors: Awa O.T. Fall, Valérie Proulle, Abibatou Sall, Alassane Mbaye, Pape Samba Ba, Maboury Diao, Moussa Seck, Macoura Gadji, Sara B. Gning, Saliou Diop, Tandakha N.D. Dièye, Blaise Félix Faye, Doudou Thiam, Marie Dreyfus

Source: Clinical Medicine Insights: Blood Disorders, Vol 2014, Iss 7, Pp 1-6 (2014)

Subject Terms: Diseases of the blood and blood-forming organs, RC633-647.5

File Description: electronic resource

Relation: http://www.la-press.com/risk-factors-for-thrombosis-in-an-african-population-article-a4158; https://doaj.org/toc/1179-545X

Access URL: https://doaj.org/article/b7f468732b1241db9cea01df5f8a3391

A thrombopoietin receptor agonist to rescue an unusual platelet transfusion-induced reaction in a p.V1316M-associated von Willebrand disease type 2B patient

Authors: Caterina Casari, Remi Favier, Paulette Legendre, Alexandre Kauskot, Frederic Adam, Veronique Picard, Peter J. Lenting, Cecile V. Denis, Valerie Proulle

Source: Therapeutic Advances in Hematology, Vol 13 (2022)

Subject Terms: Diseases of the blood and blood-forming organs, RC633-647.5

File Description: electronic resource

Relation: https://doaj.org/toc/2040-6215

Access URL: https://doaj.org/article/f46a35a8466e49af9e0fca1439be9097

Monoclonal gammopathy of clinical significance: in vivo demonstration of the anti-thrombotic effect of an acquired anti-thrombin antibody

Authors: Berenice Schell, Celine Desconclois, Xavier Mariette, Cecile Goujard, Peter J. Lenting, Cecile V. Denis, Valerie Proulle

Source: Haematologica, Vol 106, Iss 1 (2020)

Subject Terms: Diseases of the blood and blood-forming organs, RC633-647.5

File Description: electronic resource

Relation: https://haematologica.org/article/view/9910; https://doaj.org/toc/0390-6078; https://doaj.org/toc/1592-8721

Access URL: https://doaj.org/article/6272e7e6041c40748b5821b9a1e410c2

Misdiagnosis of Chronic Thrombocytopenia in Childhood.

Authors: Brigitte Bader-Meunier, Valérie Proulle, Catherine Trichet, Dominique Debray, Martine Gabolde, J. Yvart, Marie Dreyfus

Source: Journal of Pediatric Hematology/Oncology; Jul2003, Vol. 25 Issue 7, p548, 5p