Development of a novel patient reported outcome measure for health-related quality of life in amyotrophic lateral sclerosis (PROQuALS): study protocol

Authors: Jill Carlton, Philip Powell, Donna Rowen, Claire Williams, Alys Wyn Griffiths, Esther Hobson, Christopher McDermott

Source: Health and Quality of Life Outcomes, Vol 22, Iss 1, Pp 1-8 (2024)

Subject Terms: Amyotrophic lateral sclerosis (ALS), Discrete choice experiment (DCE), Health-related quality of life (HRQoL), Motor neuron disease (MND), Patient reported outcome measure (PROM), Preference-weighted measure (PWM), Computer applications to medicine. Medical informatics, R858-859.7

File Description: electronic resource

Relation: https://doaj.org/toc/1477-7525

Access URL: https://doaj.org/article/9f70e66277aa471cb2bfc1d74b204488

Advance directives in amyotrophic lateral sclerosis – a systematic review and meta-analysis

Authors: Anne Lisa Mangal, Martin Mücke, Roman Rolke, Iris Appelmann

Source: BMC Palliative Care, Vol 23, Iss 1, Pp 1-14 (2024)

Subject Terms: Amyotrophic lateral sclerosis (ALS), Motor neuron disease (MND), Advance care planning, Advance directives, Living will, Special situations and conditions, RC952-1245

File Description: electronic resource

Relation: https://doaj.org/toc/1472-684X

Access URL: https://doaj.org/article/9851dd722de5457f82e0988b581c78ff

Machine learning and brain-computer interface approaches in prognosis and individualized care strategies for individuals with amyotrophic lateral sclerosis: A systematic review

Authors: Stephanie Yen Nee Kew, Siew-Ying Mok, Choon-Hian Goh

Source: MethodsX, Vol 13, Iss , Pp 102765- (2024)

Subject Terms: Motor neuron disease (MND), Autonomic intelligence, Prognostication, Personalized, Intervention, Science

File Description: electronic resource

Relation: http://www.sciencedirect.com/science/article/pii/S2215016124002188; https://doaj.org/toc/2215-0161

Access URL: https://doaj.org/article/5af801c2db0b4054a7955cb8ee394d74

Phagocytosis of aggrecan-positive perineuronal nets surrounding motor neurons by reactive microglia expressing MMP-9 in TDP-43Q331K ALS model mice

Authors: Sang Won Cheung, Emily F. Willis, David G. Simmons, Mark C. Bellingham, Peter G. Noakes

Source: Neurobiology of Disease, Vol 200, Iss , Pp 106614- (2024)

Subject Terms: Amyotrophic lateral sclerosis (ALS), Motor neuron disease (MND), Motor neuron death, TDP-43Q331K, Perineuronal net (PNN), Aggrecan, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571

File Description: electronic resource

Relation: http://www.sciencedirect.com/science/article/pii/S0969996124002146; https://doaj.org/toc/1095-953X

Access URL: https://doaj.org/article/9b188baf16d24c7cb9c3cb629ea735bb

Tongue exercise ameliorates structural and functional upper airway deficits in a rodent model of hypoglossal motor neuron loss

Authors: Amy N. Keilholz, Ishan Pathak, Catherine L. Smith, Kate L. Osman, Lauren Smith, Grace Oti, Mojgan Golzy, Lixin Ma, Teresa E. Lever, Nicole L. Nichols

Source: Frontiers in Neurology, Vol 15 (2024)

Subject Terms: motor neuron disease (MND), breathing, respiration, dysphagia, degeneration, rat model, Neurology. Diseases of the nervous system, RC346-429

File Description: electronic resource

Relation: https://www.frontiersin.org/articles/10.3389/fneur.2024.1441529/full; https://doaj.org/toc/1664-2295

Access URL: https://doaj.org/article/bd704596fda541c590c6727ea41c2f81

Effect of ultrasound-mediated blood-spinal cord barrier opening on survival and motor function in females in an amyotrophic lateral sclerosis mouse modelResearch in context

Authors: Anne-Sophie Montero, Ilyes Aliouat, Matthieu Ribon, Michael Canney, Lauriane Goldwirt, Samia Mourah, Félix Berriat, Christian S. Lobsiger, Pierre-François Pradat, François Salachas, Gaëlle Bruneteau, Alexandre Carpentier, Séverine Boillée

Source: EBioMedicine, Vol 106, Iss , Pp 105235- (2024)

Subject Terms: Blood-spinal cord barrier (BSCB), Ultrasound, Amyotrophic lateral sclerosis (ALS), Motor neuron disease (MND), Lymphocytes, Neuroinflammation, Medicine, Medicine (General), R5-920

File Description: electronic resource

Relation: http://www.sciencedirect.com/science/article/pii/S2352396424002706; https://doaj.org/toc/2352-3964

Access URL: https://doaj.org/article/829c21513bc04088ba5edb899d13fb89

A Self-Governing Wheelchair for Severely Disabled Patients in an Indoor Environment Utilizing EEG and Laser Technologies

Authors: Bharali, Sanjeeb, Mathi, Shyamala, Dash, Pooja, Chandra, Sharath, Chavan, Bhushan

Source: 2018 International Conference on Emerging Trends and Innovations In Engineering And Technological Research (ICETIETR) Emerging Trends and Innovations In Engineering And Technological Research (ICETIETR), 2018 International Conference on. :1-5 Jul, 2018

Relation: 2018 International Conference on Emerging Trends and Innovations In Engineering And Technological Research (ICETIETR)

Neuronal dysfunction caused by FUSR521G promotes ALS-associated phenotypes that are attenuated by NF-κB inhibition

Authors: Mari Carmen Pelaez, Antoine Desmeules, Pauline A. Gelon, Bastien Glasson, Laetitia Marcadet, Alicia Rodgers, Daniel Phaneuf, Silvia Pozzi, Paul A. Dutchak, Jean-Pierre Julien, Chantelle F. Sephton

Source: Acta Neuropathologica Communications, Vol 11, Iss 1, Pp 1-21 (2023)

Subject Terms: Amyotrophic lateral sclerosis (ALS), Frontotemporal dementia (FTD), Motor neuron disease (MND), Synapse, Dendrite, Synaptopathy, Neurology. Diseases of the nervous system, RC346-429

File Description: electronic resource

Relation: https://doaj.org/toc/2051-5960

Access URL: https://doaj.org/article/7607d7cbde0a4784a3e433fdc4157ae9

A Simplified Approach to Assist Severely Disabled Patients to Make a Self-Governing Movement Utilizing EEG and EOG Technique

Authors: Bharali, Sanjeeb, Chandra, Sharath, Dash, Pooja, Chavan, Bhushan

Source: 2018 Second International Conference on Electronics, Communication and Aerospace Technology (ICECA) Electronics, Communication and Aerospace Technology (ICECA), 2018 Second International Conference on. :216-220 Mar, 2018

Relation: 2018 Second International conference on Electronics, Communication and Aerospace Technology (ICECA)

Neuroimaging findings in preclinical amyotrophic lateral sclerosis models—How well do they mimic the clinical phenotype? A systematic review

Authors: Amelia Elaine Cannon, Wolfgang Emanuel Zürrer, Charlotte Zejlon, Zsolt Kulcsar, Sebastian Lewandowski, Fredrik Piehl, Tobias Granberg, Benjamin Victor Ineichen

Source: Frontiers in Veterinary Science, Vol 10 (2023)

Subject Terms: motor neuron disease (MND), magnetic resonance imaging (MRI), systematic review, amyotrophic lateral sclerosis, neuroimaging, external validity, Veterinary medicine, SF600-1100

File Description: electronic resource

Relation: https://www.frontiersin.org/articles/10.3389/fvets.2023.1135282/full; https://doaj.org/toc/2297-1769

Access URL: https://doaj.org/article/c10a124cd8ff4a4fbd69c22720c06a70

Atypical motor neuron disease variant: facial-onset sensory and motor neuronopathy syndrome (FOSMN)

Authors: Betül Özenç, Zeki Odabaşı, Ersin Tan

Source: The Egyptian Journal of Neurology, Psychiatry and Neurosurgery, Vol 58, Iss 1, Pp 1-3 (2022)

Subject Terms: FOSMN, Neuronopathy, Dysphagia, Motor neuron disease (MND), Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571

File Description: electronic resource

Relation: https://doaj.org/toc/1687-8329

Access URL: https://doaj.org/article/2da936daefa64d618e764621b26f2e16

Phenotypic correlates of serum neurofilament light chain levels in amyotrophic lateral sclerosis

Authors: Federico Verde, Ilaria Milone, Eleonora Colombo, Alessio Maranzano, Federica Solca, Silvia Torre, Alberto Doretti, Francesco Gentile, Arianna Manini, Ruggero Bonetti, Silvia Peverelli, Stefano Messina, Luca Maderna, Claudia Morelli, Barbara Poletti, Antonia Ratti, Vincenzo Silani, Nicola Ticozzi

Source: Frontiers in Aging Neuroscience, Vol 15 (2023)

Subject Terms: amyotrophic lateral sclerosis (ALS), motor neuron disease (MND), neurofilament light chain (NFL), axon, biomarker, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571

File Description: electronic resource

Relation: https://www.frontiersin.org/articles/10.3389/fnagi.2023.1132808/full; https://doaj.org/toc/1663-4365

Access URL: https://doaj.org/article/d1ff32eb10ce42839bc554c47893310c

Synaptic dysfunction in ALS and FTD: anatomical and molecular changes provide insights into mechanisms of disease

Authors: Pauline A. Gelon, Paul A. Dutchak, Chantelle F. Sephton

Source: Frontiers in Molecular Neuroscience, Vol 15 (2022)

Subject Terms: amyotrophic lateral sclerosis (ALS, Lou Gehrig Disease), frontotemporal dementia (FTD), motor neuron disease (MND), synapse, dendrite, C9ORF72, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571

File Description: electronic resource

Relation: https://www.frontiersin.org/articles/10.3389/fnmol.2022.1000183/full; https://doaj.org/toc/1662-5099

Access URL: https://doaj.org/article/0ac74559071c4373822be26e63358b9a

Suppression of the necroptotic cell death pathways improves survival in Smn2B/− mice

Authors: Lucia Chehade, Marc-Olivier Deguise, Yves De Repentigny, Rebecca Yaworski, Ariane Beauvais, Sabrina Gagnon, Niko Hensel, Rashmi Kothary

Source: Frontiers in Cellular Neuroscience, Vol 16 (2022)

Subject Terms: neuroinflammation, necroptosis, motor neuron disease (MND), multi-system disease, mouse genetic models, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571

File Description: electronic resource

Relation: https://www.frontiersin.org/articles/10.3389/fncel.2022.972029/full; https://doaj.org/toc/1662-5102

Access URL: https://doaj.org/article/7012f123c6254c638026160eccd82345

Profiling morphologic MRI features of motor neuron disease caused by TARDBP mutations

Authors: Edoardo Gioele Spinelli, Alma Ghirelli, Nilo Riva, Elisa Canu, Veronica Castelnovo, Teuta Domi, Laura Pozzi, Paola Carrera, Vincenzo Silani, Adriano Chiò, Massimo Filippi, Federica Agosta

Source: Frontiers in Neurology, Vol 13 (2022)

Subject Terms: motor neuron disease (MND), amyotrophic lateral sclerosis (ALS), transactive response (TAR) DNA binding protein 43 (TARDBP), magnetic resonance imaging (MRI), voxel-based morphometry (VBM), Neurology. Diseases of the nervous system, RC346-429

File Description: electronic resource

Relation: https://www.frontiersin.org/articles/10.3389/fneur.2022.931006/full; https://doaj.org/toc/1664-2295

Access URL: https://doaj.org/article/6047c59f82b24d8bb3680aaeef13b7bb

A Strength Endurance Exercise Paradigm Mitigates Deficits in Hypoglossal-Tongue Axis Function, Strength, and Structure in a Rodent Model of Hypoglossal Motor Neuron Degeneration

Authors: Erika R. Murphy, Rebecca Thompson, Kate L. Osman, Chandler Haxton, Margaret Brothers, Li Lee, Kristen Warncke, Catherine L. Smith, Amy N. Keilholz, Ali Hamad, Mojgan Golzy, Filiz Bunyak, Lixin Ma, Nicole L. Nichols, Teresa E. Lever

Source: Frontiers in Neuroscience, Vol 16 (2022)

Subject Terms: motor neuron disease (MND), hypoglossal, tongue, dysphagia, exercise, rodent model, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571

File Description: electronic resource

Relation: https://www.frontiersin.org/articles/10.3389/fnins.2022.869592/full; https://doaj.org/toc/1662-453X

Access URL: https://doaj.org/article/42cced8f5f0544f0b16bc704e7fb0608

Parkinsonian Syndromes in Motor Neuron Disease: A Clinical Study

Authors: Jacopo Pasquini, Francesca Trogu, Claudia Morelli, Barbara Poletti, Floriano Girotti, Silvia Peverelli, Alberto Brusati, Antonia Ratti, Andrea Ciammola, Vincenzo Silani, Nicola Ticozzi

Source: Frontiers in Aging Neuroscience, Vol 14 (2022)

Subject Terms: motor neuron disease (MND), parkinsonism, amyotrophic lateral sclerosis, primary lateral sclerosis (PLS), progressive supranuclear palsy, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571

File Description: electronic resource

Relation: https://www.frontiersin.org/articles/10.3389/fnagi.2022.917706/full; https://doaj.org/toc/1663-4365

Access URL: https://doaj.org/article/fa7507a65a6849e0a1c54ec94b5e07c8

Breached Barriers: A Scoping Review of Blood-Central Nervous System Barrier Pathology in Amyotrophic Lateral Sclerosis

Authors: Ario Mirian, Alexander Moszczynski, Serena Soleimani, Isabelle Aubert, Lorne Zinman, Agessandro Abrahao

Source: Frontiers in Cellular Neuroscience, Vol 16 (2022)

Subject Terms: blood-brain barrier, blood-spinal cord barrier (BSCB), motor neuron disease (MND), amyotrophic lateral sclerosis, neurovascular unit, pericyte, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571

File Description: electronic resource

Relation: https://www.frontiersin.org/articles/10.3389/fncel.2022.851563/full; https://doaj.org/toc/1662-5102

Access URL: https://doaj.org/article/fa37cd7e9118445a84813745969b87e0

Motor Neuron Diseases and Neuroprotective Peptides: A Closer Look to Neurons

Authors: Emanuela Zuccaro, Diana Piol, Manuela Basso, Maria Pennuto

Source: Frontiers in Aging Neuroscience, Vol 13 (2021)

Subject Terms: motor neuron (MN), IGF-1 (insulin-like growth factor 1), PACAP (pituitary adenylate cyclase-activating polypeptide), motor neuron disease (MND), ALS (Amyotrophic lateral sclerosis), spinobulbar muscular atrophy (SBMA), Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571

File Description: electronic resource

Relation: https://www.frontiersin.org/articles/10.3389/fnagi.2021.723871/full; https://doaj.org/toc/1663-4365

Access URL: https://doaj.org/article/140e54cf59e24f8181d10beb6754d262

The Role of Mitochondria, Oxidative Stress and Altered Calcium Homeostasis in Amyotrophic Lateral Sclerosis: From Current Developments in the Laboratory to Clinical Treatments

Authors: Manoj Kumar Jaiswal

Subject Terms: RC321-571, Q1-390, Mitochondria, neurodegenerative disease, Ca2+ signaling, multidrug therapy, Amyotrophic lateral sclerosis (ALS), Superoxide dismutase 1 (SOD1), Motor neuron disease (MND), excitotoxicity, Riluzole, multifactorial disease, Neurosciences

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Relation: Frontiers Research Topics

Access URL: https://directory.doabooks.org/handle/20.500.12854/58592
http://www.frontiersin.org/books/The_Role_of_Mitochondria_Oxidative_Stress_and_Altered_Calcium_Homeostasis_in_Amyotrophic_Lateral_Sc/1171#nogo
http://journal.frontiersin.org/researchtopic/1909/the-role-of-mitochondria-oxidative-stress-and-altered-calcium-homeostasis-in-amyotrophic-lateral-scl