Respiratory pathology in the Optn-/- mouse model of Amyotrophic Lateral Sclerosis

Authors: McCall, Angela L., Dhindsa, Justin S., Pucci, Logan A., Kahn, Amanda F., Fusco, Anna F., Biswas, Debolina D., Strickland, Laura M., Tseng, Henry C., ElMallah, Mai K. ^*

Source: In Respiratory Physiology & Neurobiology November 2020 282

Intralingual Administration of AAVrh10-miRSOD1 Improves Respiratory But Not Swallowing Function in a Superoxide Dismutase-1 Mouse Model of Amyotrophic Lateral Sclerosis

Authors: Lind, Lori A., Andel, Ellyn M., McCall, Angela L., Dhindsa, Justin S., Johnson, Katherine A., Stricklin, Olivia E., Mueller, Christian, ElMallah, Mai K., Lever, Teresa E., Nichols, Nicole L.

Source: Human gene therapy. 31(15/16):828-838

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Reduction of Autophagic Accumulation in Pompe Disease Mouse Model Following Gene Therapy

Authors: McCall, Angela L., Stankov, Sylvia G., Cowen, Gabrielle, Cloutier, Denise, Zhang, Zizhao, Yang, Lin, Clement, Nathalie, Falk, Darin J., Byrne, Barry J.

Source: Current gene therapy. 19(3):197-207

Availability: http://explore.bl.uk/primo_library/libweb/action/display.do?tabs=detailsTab&gathStatTab=true&ct=display&fn=search&doc=ETOCvdc_100090525262.0x000001&indx=1&recIds=ETOCvdc_100090525262.0x000001

Systemic Delivery of AAVB1-GAA Clears Glycogen and Prolongs Survival in a Mouse Model of Pompe Disease

Authors: Keeler, Allison M., Zieger, Marina, Todeasa, Sophia H., McCall, Angela L., Gifford, Jennifer C., Birsak, Samantha, Choudhury, Sourav R., Byrne, Barry J., Sena-Esteves, Miguel, ElMallah, Mai K.

Source: Human gene therapy. 30(1):57-68

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Corrigendum to 'Respiratory pathology in the optn-/- mouse model of amyotrophic lateral sclerosis' [Respir. Physiol. Neurobiol. 282 (2020) 103525]

Authors: McCall, Angela L., Dhindsa, Justin S., Pucci, Logan A., Khan, Amanda F., Fusco, Anna F., Biswas, Debolina D., Strickland, Laura M., Tseng, Henry C., ElMallah, Mai K.

Source: Respiratory physiology & neurobiology. 284

Availability: http://explore.bl.uk/primo_library/libweb/action/display.do?tabs=detailsTab&gathStatTab=true&ct=display&fn=search&doc=ETOCvdc_100117786683.0x000001&indx=1&recIds=ETOCvdc_100117786683.0x000001

Motor axonopathies in a mouse model of Duchenne muscular dystrophy.

Authors: Dhindsa, Justin S.¹, McCall, Angela L.¹, Strickland, Laura M.¹, Fusco, Anna F.¹, Kahn, Amanda F.¹, ElMallah, Mai K.¹ mai.elmallah@duke.edu

Source: Scientific Reports. 6/2/2020, Vol. 10 Issue 1, p1-7. 7p.

Subject Terms: *DUCHENNE muscular dystrophy, *NEUROMUSCULAR diseases, *DYSTROPHIN, *SKELETAL muscle, *NEUROLOGICAL disorders, *LABORATORY mice

Mavis Agbandje-McKenna's Lifelong Commitment to Teaching and Research

Authors: Byrne, Barry J., McCall, Angela L., Davidson, Beverly L., Samulski, R. Jude

Source: Human gene therapy. 32(7/8):319-320

Availability: http://explore.bl.uk/primo_library/libweb/action/display.do?tabs=detailsTab&gathStatTab=true&ct=display&fn=search&doc=ETOCvdc_100152113899.0x000001&indx=1&recIds=ETOCvdc_100152113899.0x000001

Glycogen accumulation in smooth muscle in the Pompe disease mouse

Authors: McCall, Angela L., Dhinsda, Justin S., Zheng, Lucy, Bailey, Aidan M., Strickland, Laura M., ElMallah, Mai K.

Source: Molecular genetics and metabolism. 132(2):S70-S70

Availability: http://explore.bl.uk/primo_library/libweb/action/display.do?tabs=detailsTab&gathStatTab=true&ct=display&fn=search&doc=ETOCvdc_100135065453.0x000001&indx=1&recIds=ETOCvdc_100135065453.0x000001

Motor Neuron Pathology Leads to Respiratory Deficiency in Optn−/− Mice

Authors: McCall, Angela L., Dhindsa, Justin S., Pucci, Logan A., Strickland, Laura M., Kahn, Amanda F., Fusco, Anna F., Tseng, Henry, ElMallah, Mai K.

Source: FASEB journal. 34(S1):1-1

Availability: http://explore.bl.uk/primo_library/libweb/action/display.do?tabs=detailsTab&gathStatTab=true&ct=display&fn=search&doc=ETOCvdc_100140421089.0x000001&indx=1&recIds=ETOCvdc_100140421089.0x000001

Respiratory Dysfunction in a Mouse Model of Spinocerebellar Ataxia 7

Authors: Fusco, Anna F., Pucci, Logan, McCall, Angela L., Dhindsa, Justin, Kahn, Amanda, Switonski, Pawel, Strickland, Laura, Spada, Albert La, ElMallah, Mai K.

Source: FASEB journal. 34(S1):1-1

Availability: http://explore.bl.uk/primo_library/libweb/action/display.do?tabs=detailsTab&gathStatTab=true&ct=display&fn=search&doc=ETOCvdc_100140410701.0x000001&indx=1&recIds=ETOCvdc_100140410701.0x000001

Respiratory Dysfunction in a novel mouse model of Duchenne Muscular Dystrophy.

Authors: McCall, Angela L., Bailey, Aidan M., Pucci, Logan A., Dhindsa, Justin S., Strickland, Laura M., Robinson-Hamm, Jacqueline, Gersbach, Charles A., ElMallah, Mai K.

Source: FASEB journal. 34(S1):1-1

Availability: http://explore.bl.uk/primo_library/libweb/action/display.do?tabs=detailsTab&gathStatTab=true&ct=display&fn=search&doc=ETOCvdc_100140409238.0x000001&indx=1&recIds=ETOCvdc_100140409238.0x000001

Intralingual Administration of AAVrh10-miR^SOD1 Improves Respiratory But Not Swallowing Function in a Superoxide Dismutase-1 Mouse Model of Amyotrophic Lateral Sclerosis.

Authors: Lind, Lori A., Andel, Ellyn M., McCall, Angela L., Dhindsa, Justin S., Johnson, Katherine A., Stricklin, Olivia E., Mueller, Christian, ElMallah, Mai K., Lever, Teresa E., Nichols, Nicole L.

Source: Human Gene Therapy; Aug2020, Vol. 31 Issue 15-16, p828-838, 11p

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382. Correction of Autophagic Dysregulation in Pompe Disease Following Gene Therapy

Authors: McCall, Angela L., Stankov, Sylvia G., Falk, Darin J., Byrne, Barry J.

Source: Molecular therapy. 24(S1):S152-S152

Availability: http://explore.bl.uk/primo_library/libweb/action/display.do?tabs=detailsTab&gathStatTab=true&ct=display&fn=search&doc=ETOCvdc_100081833330.0x000001&indx=1&recIds=ETOCvdc_100081833330.0x000001

The Respiratory Phenotype of Pompe Disease Mouse Models.

Authors: Fusco, Anna F.¹ (AUTHOR) anna.fusco@duke.edu, McCall, Angela L.¹ (AUTHOR), Dhindsa, Justin S.¹ (AUTHOR), Zheng, Lucy¹ (AUTHOR), Bailey, Aidan¹ (AUTHOR), Kahn, Amanda F.¹ (AUTHOR), ElMallah, Mai K.¹ (AUTHOR) mai.elmallah@duke.edu

Source: International Journal of Molecular Sciences. Mar2020, Vol. 21 Issue 6, p2256. 1p.

Subject Terms: *GLYCOGEN storage disease type II, *HYPOGLOSSAL nerve, *GLYCOGEN storage disease, *MOUSE diseases, *PHRENIC nerve, *MYONEURAL junction

Macroglossia, Motor Neuron Pathology, and Airway Malacia Contribute to Respiratory Insufficiency in Pompe Disease: A Commentary on Molecular Pathways and Respiratory Involvement in Lysosomal Storage Diseases.

Authors: McCall, Angela L.¹ angela.mccall440@duke.edu, ElMallah, Mai K.¹ mai.elmallah@duke.edu

Source: International Journal of Molecular Sciences. Feb2019, Vol. 20 Issue 3, p751. 1p.

Subject Terms: *RESPIRATORY organ abnormalities, *SALIVA

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Respiratory dysfunction in a mouse model of spinocerebellar ataxia type 7

Authors: Fusco, Anna F., Pucci, Logan A., Switonski, Pawel M., Biswas, Debolina D., McCall, Angela L., Kahn, Amanda F., Dhindsa, Justin S., Strickland, Laura M., La Spada, Albert R., ElMallah, Mai K.

Source: Disease Models and Mechanisms; July 2021, Vol. 14 Issue: 7 pdmm048893-dmm048893, 1p

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