Concordance of cerebrospinal fluid real‐time quaking‐induced conversion across the European Creutzfeldt–Jakob Disease Surveillance Network

Authors: McKenzie, Neil, Piconi, Gabriele, Culeux, Audrey, Hammarin, Anna‐Lena, Stergiou, Christos, Tzartos, Socrates, Versleijen, Alexandra A. M., Geer, Jacqueline, Cras, Patrick, Cardone, Franco, Ladogana, Anna, Mannana, Angela, Rossi, Marcello, Bongianni, Matilde, Perra, Daniela, Regelsberger, Guenther, Klotz, Sigrid, Hornemann, Simone, Aguzzi, Adriano, Schmitz, Matthias, Andrews, Mary, Burns, Kimberley, Haïk, Stéphane, Ruiz‐García, Raquel, Verner‐Carlsson, Jenny, Tzartos, John, Verbeek, Marcel M., Vil, Bart, Poleggi, Anna, Parchi, Piero, Zanusso, Gianluigi, Gelpi, Ellen, Frontzek, Karl, Reimann, Regina, Hermann, Peter, Zerr, Inga, Pal, Suvankar, Green, Alison

Source: European journal of neurology. 29(8):2431-2438

Availability: http://explore.bl.uk/primo_library/libweb/action/display.do?tabs=detailsTab&gathStatTab=true&ct=display&fn=search&doc=ETOCvdc_100156044198.0x000001&indx=1&recIds=ETOCvdc_100156044198.0x000001

Neuroprotective Effect of Withaferin Derivatives toward MPP⁺ and 6‑OHDA Toxicity to Dopaminergic Neurons.

Authors: Parrales, Valeria, Arcile, Guillaume, Laserre, Louise, Normant, Sébastien, Le Goff, Géraldine, Da Costa Noble, Christian, Ouazzani, Jamal, Callizot, Noelle, Haïk, Stéphane, Rabhi, Chérif, Bizat, Nicolas

Source: ACS Chemical Neuroscience; 3/5/2025, Vol. 16 Issue 5, p802-817, 16p

Demyelinating neuropathy as the initial presentation of familial E200K Creutzfeldt–Jakob disease in two patients.

Authors: Delorme, Cécile, Pégat, Antoine, Theuriet, Julian, Brandel, Jean‐Philippe, Roze, Emmanuel, Viala, Karine, Zyss, Julie, Thobois, Stéphane, Fourier, Anthony, Bernard, Emilien, Svahn, Juliette, Laurencin, Chloé, Jaulent, Paul, Vandendries, Christophe, Quadrio, Isabelle, Desestret, Virginie, Meyronet, David, Maisonobe, Thierry, Haïk, Stéphane, Seilhean, Danielle

Source: Annals of Clinical & Translational Neurology; Mar2025, Vol. 12 Issue 3, p653-658, 6p

Doxycycline inhibits α-synuclein-associated pathologies in vitro and in vivo

Authors: Dominguez-Meijide, Antonio, Parrales, Valeria, Vasili, Eftychia, González-Lizárraga, Florencia, König, Annekatrin, Lázaro, Diana F., Lannuzel, Annie, Haik, Stéphane, Del Bel, Elaine, Chehín, Rosana, Raisman-Vozari, Rita, Michel, Patrick P., Bizat, Nicolas, Outeiro, Tiago Fleming

Source: In Neurobiology of Disease April 2021 151

Biomarkers and diagnostic guidelines for sporadic Creutzfeldt-Jakob disease

Authors: Hermann, Peter ^*, Appleby, Brian, Brandel, Jean-Philippe, Caughey, Byron, Collins, Steven, Geschwind, Michael D, Green, Alison, Haïk, Stephane, Kovacs, Gabor G, Ladogana, Anna, Llorens, Franc, Mead, Simon, Nishida, Noriyuki, Pal, Suvankar, Parchi, Piero, Pocchiari, Maurizio, Satoh, Katsuya, Zanusso, Gianluigi, Zerr, Inga

Source: In The Lancet Neurology March 2021 20(3):235-246

Identification of novel risk loci and causal insights for sporadic Creutzfeldt-Jakob disease: a genome-wide association study

Authors: Jones, Emma, Hummerich, Holger, Viré, Emmanuelle, Uphill, James, Dimitriadis, Athanasios, Speedy, Helen, Campbell, Tracy, Norsworthy, Penny, Quinn, Liam, Whitfield, Jerome, Linehan, Jacqueline, Jaunmuktane, Zane, Brandner, Sebastian, Jat, Parmjit, Nihat, Akin, How Mok, Tze, Ahmed, Parvin, Collins, Steven, Stehmann, Christiane, Sarros, Shannon, Kovacs, Gabor G, Geschwind, Michael D, Golubjatnikov, Aili, Frontzek, Karl, Budka, Herbert, Aguzzi, Adriano, Karamujić-Čomić, Hata, van der Lee, Sven J, Ibrahim-Verbaas, Carla A, van Duijn, Cornelia M, Sikorska, Beata, Golanska, Ewa, Liberski, Pawel P, Calero, Miguel, Calero, Olga, Sanchez-Juan, Pascual, Salas, Antonio, Martinón-Torres, Federico, Bouaziz-Amar, Elodie, Haïk, Stéphane, Laplanche, Jean-Louis, Brandel, Jean-Phillipe, Amouyel, Phillipe, Lambert, Jean-Charles, Parchi, Piero, Bartoletti-Stella, Anna, Capellari, Sabina, Poleggi, Anna, Ladogana, Anna, Pocchiari, Maurizio, Aneli, Serena, Matullo, Giuseppe, Knight, Richard, Zafar, Saima, Zerr, Inga, Booth, Stephanie, Coulthart, Michael B, Jansen, Gerard H, Glisic, Katie, Blevins, Janis, Gambetti, Pierluigi, Safar, Jiri, Appleby, Brian, Collinge, John, Mead, Simon ^*

Source: In The Lancet Neurology October 2020 19(10):840-848

Potential human transmission of amyloid β pathology: surveillance and risks

Authors: Lauwers, Elsa, Lalli, Giovanna, Brandner, Sebastian, Collinge, John, Compernolle, Veerle, Duyckaerts, Charles, Edgren, Gustaf, Haïk, Stéphane, Hardy, John, Helmy, Adel, Ivinson, Adrian J, Jaunmuktane, Zane, Jucker, Mathias, Knight, Richard, Lemmens, Robin, Lin, I-Chun, Love, Seth, Mead, Simon, Perry, V Hugh, Pickett, James, Poppy, Guy, Radford, Sheena E, Rousseau, Frederic, Routledge, Carol, Schiavo, Giampietro, Schymkowitz, Joost, Selkoe, Dennis J, Smith, Colin, Thal, Dietmar R, Theys, Tom, Tiberghien, Pierre, van den Burg, Peter, Vandekerckhove, Philippe, Walton, Clare, Zaaijer, Hans L, Zetterberg, Henrik, De Strooper, Bart ^*

Source: In The Lancet Neurology October 2020 19(10):872-878

Prion-like properties of Tau assemblies

Authors: Clavaguera, Florence, Duyckaerts, Charles, Haïk, Stéphane

Source: In Current Opinion in Neurobiology April 2020 61:49-57

Ring trial of 2nd generation RT‐QuIC diagnostic tests for sporadic CJD

Authors: Orrú, Christina D., Groveman, Bradley R., Foutz, Aaron, Bongianni, Matilde, Cardone, Franco, McKenzie, Neil, Culeux, Audrey, Poleggi, Anna, Grznarova, Katarina, Perra, Daniela, Fiorini, Michele, Liu, Xiaoqin, Ladogana, Anna, Sbriccoli, Marco, Hughson, Andrew G., Haïk, Stéphane, Green, Alison J., Geschwind, Michael D., Pocchiari, Maurizio, Safar, Jiri G., Zanusso, Gianluigi, Caughey, Byron

Source: Annals of clinical and translational neurology. 7(11):2262-2271

Availability: http://explore.bl.uk/primo_library/libweb/action/display.do?tabs=detailsTab&gathStatTab=true&ct=display&fn=search&doc=ETOCvdc_100109990406.0x000001&indx=1&recIds=ETOCvdc_100109990406.0x000001

Automated deep learning segmentation of neuritic plaques and neurofibrillary tangles in Alzheimer disease brain sections using a proprietary software.

Authors: Ingrassia, Lea, Boluda, Susana, Potier, Marie-Claude, Haïk, Stéphane, Jimenez, Gabriel, Kar, Anuradha, Racoceanu, Daniel, Delatour, Benoît, Stimmer, Lev

Source: Journal of Neuropathology & Experimental Neurology; Sep2024, Vol. 83 Issue 9, p752-762, 11p

Region-specific protein misfolding cyclic amplification reproduces brain tropism of prion strains

Authors: Privat, Nicolas, Levavasseur, Etienne, Yildirim, Serfildan, Hannaoui, Samia, Brandel, Jean-Philippe, Laplanche, Jean-Louis ^**, Béringue, Vincent, Seilhean, Danielle, Haïk, Stéphane

Source: In Journal of Biological Chemistry 6 October 2017 292(40):16688-16696

Prions et transconformation protéique: une perspective historique

Alternate Title: History of Prions and transmission of protein misfolding (English)

Authors: Hauw, Jean-Jacques ^*, HaÏk, Stéphane ^**, Brandel, Jean-Philippe ^***

Source: In Bulletin de l'Académie Nationale de Médecine June 2015 199(6):787-796

Neuropathology of iatrogenic Creutzfeldt–Jakob disease and immunoassay of French cadaver-sourced growth hormone batches suggest possible transmission of tauopathy and long incubation periods for the transmission of Abeta pathology

Authors: Duyckaerts, Charles, Sazdovitch, Véronique, Ando, Kunie, Seilhean, Danielle, Privat, Nicolas, Yilmaz, Zehra, Peckeu, Laurène, Amar, Elodie, Comoy, Emmanuel, Maceski, Aleksandra, Lehmann, Sylvain, Brion, Jean-Pierre, Brandel, Jean-Philippe, Haïk, Stéphane

Source: Acta neuropathologica. 135(2):201-212

Availability: http://explore.bl.uk/primo_library/libweb/action/display.do?tabs=detailsTab&gathStatTab=true&ct=display&fn=search&doc=ETOCvdc_100141526220.0x000001&indx=1&recIds=ETOCvdc_100141526220.0x000001

Cycline Efficacy on the Propagation of Human Prions in Primary Cultured Neurons is Strain-Specific

Authors: Hannaoui, Samia, Gougerot, Alexianne, Privat, Nicolas, Levavasseur, Etienne, Bizat, Nicolas, Hauw, Jean-Jacques, Brandel, Jean-Philippe, Haïk, Stéphane

Source: The Journal of Infectious Diseases, 2014 Apr 01. 209(7), 1144-1148.

Access URL: http://www.jstor.org/stable/43708439

Doxycycline in Creutzfeldt-Jakob disease: a phase 2, randomised, double-blind, placebo-controlled trial

Authors: Haïk, Stéphane, Marcon, Gabriella, Mallet, Alain, Tettamanti, Mauro, Welaratne, Arlette, Giaccone, Giorgio, Azimi, Shohreh, Pietrini, Vladimiro, Fabreguettes, Jean-Roch, Imperiale, Daniele, Cesaro, Pierre, Buffa, Carlo, Aucan, Christophe, Lucca, Ugo, Peckeu, Laurène, Suardi, Silvia, Tranchant, Christine, Zerr, Inga, Houillier, Caroline, Redaelli, Veronica, Vespignani, Hervé, Campanella, Angela, Sellal, François, Krasnianski, Anna, Seilhean, Danielle, Heinemann, Uta, Sedel, Frédéric, Canovi, Mara, Gobbi, Marco, Di Fede, Giuseppe, Laplanche, Jean-Louis, Pocchiari, Maurizio, Salmona, Mario, Forloni, Gianluigi, Brandel, Jean-Philippe, Tagliavini, Fabrizio

Source: In Lancet Neurology February 2014 13(2):150-158

Validation of the Medical Research Council prion disease rating scale in France.

Authors: Brandel, Jean-Philippe, Welaratne, Arlette, Denouel, Angeline, Haïk, Stéphane

Source: Brain Communications; 2023, Vol. 5 Issue 6, p1-6, 6p

Introduction : Prions et transconformation protéique: une perspective historique

Authors: Hauw, Jean-Jacques, Haïk, Stéphane, Brandel, Jean-Philippe

Source: Bulletin de l'Académie nationale de médecine.é. 199(6):787-796

Availability: http://explore.bl.uk/primo_library/libweb/action/display.do?tabs=detailsTab&gathStatTab=true&ct=display&fn=search&doc=ETOCRN608392772&indx=1&recIds=ETOCRN608392772

Tau-positive grains are constant in centenarians’ hippocampus

Authors: Pham, Chi-Tuan, de Silva, Rohan, Haïk, Stéphane, Verny, Marc, Sachet, Annick, Forette, Bernard, Lees, Andrew, Hauw, Jean-Jacques, Duyckaerts, Charles

Source: In Neurobiology of Aging 2011 32(7):1296-1303

The Pesticide Chlordecone Promotes Parkinsonism-like Neurodegeneration with Tau Lesions in Midbrain Cultures and C. elegans Worms.

Authors: Parrales-Macias, Valeria, Michel, Patrick P., Tourville, Aurore, Raisman-Vozari, Rita, Haïk, Stéphane, Hunot, Stéphane, Bizat, Nicolas, Lannuzel, Annie

Source: Cells (2073-4409); May2023, Vol. 12 Issue 9, p1336, 24p

Subject Terms: CAENORHABDITIS elegans, CHLORDECONE, MESENCEPHALON, DOPAMINERGIC neurons, ORGANOCHLORINE pesticides, TAU proteins, CELL culture, DOPAMINE receptors

Human prion diseases: from antibody screening to a standardized fast immunodiagnosis using automation

Authors: Privat, Nicolas, Laffont-Proust, Isabelle, Faucheux, Baptiste A, Sazdovitch, Véronique, Frobert, Yveline, Laplanche, Jean-Louis, Grassi, Jacques, Hauw, Jean-Jacques, Haïk, Stéphane

Source: In Modern Pathology February 2008 21(2):140-149