Vanzacaftor–tezacaftor–deutivacaftor versus elexacaftor–tezacaftor–ivacaftor in individuals with cystic fibrosis aged 12 years and older (SKYLINE Trials VX20-121-102 and VX20-121-103): results from two randomised, active-controlled, phase 3 trials

Authors: Krick, Stefanie, McCoy, Karen, Goss, Christopher, Weiner, Daniel, Billings, Joanne, Ren, Clement, Atkinson, Jeffrey, Linnemann, Rachel, Trimble, Aaron, Frederick, Carla, Liou, Theodore, Escobar, Hugo, Wang, Janice, Deschamps, Ashley, Froh, Deborah, Chmiel, James, Wurth, Mark, Yonker, Lael, Jain, Manu, Millard, Susan, Tolle, James, Filbrun, Amy, Taylor-Cousar, Jennifer, Ruiz, Fadel, Brown, Cynthia, Quick, Bryon, Brown, Perry, Kennedy, John, Ruddy, Jennifer, Shkolnik, Boris, Pancham, Krishna, DiMango, Emily, Fiel, Stanley, Mueller, Gary, Livingston, Floyd, Braun, Andrew, O'Sullivan, Brian, Dubin, Patricia, Teneback, Charlotte, Kremer, Ted, Welter, John, Hoppe, Jordana, Jain, Raksha, Calimano, Francisco, Johannes, Jimmy, Daines, Cori, Green, Deanna, Keens, Thomas, Trillo-Alvarez, Cesar, Scher, Herschel, Mermis, Joel, Morrissey, Brian, Wallace, James, Barrios, Christopher, Callison, John, Holliday, Zachary, Klingsberg, Ross, Efrati, Ori, Cohen-Cymberknoh, Malena, Prais, Dario, Azevedo, Pilar, Quintana-Gallego, Esther, Wong, Janice, Mondejar-Lopez, Pedro, Lopez Neyra, Alejandro, Amorim, Adelina, Sivam, Sheila, Asensio de la Cruz, Oscar, Waller, Michael, Forseen, Caralee, Marion, Chad, Dittrich, Anna-Maria, Lysinger, Jerimiah, Casserly, Brian, Luna, Carmen, Brown, Sarah, Singer, Jonathan, Schellhase, Dennis, Roberts, Jon, King, Christopher, Byrnes, Catherine, Ringshausen, Felix, Hebestreit, Helge, Lorenz, Michael, Ruppel, Renate, Drevinek, Pavel, Dillenhofer, Stefanie, Stahl, Mirjam, Gleiber, Wolfgang, Homola, Lukas, Naehrig, Susanne, Stehling, Florian, Sutharsan, Sivagurunathan, Fischer, Rainald, Poplawska, Krystyna, Haworth, Charles, Simmonds, Nicholas, Urquhart, Don, Duckers, Jamie, Carroll, Mary, Barry, Peter, Doe, Simon, Hilliard, Tom, MacGregor, Gordon, Patel, Neil, Withers, Nicholas, Peckham, Daniel, Ledson, Martin, Koser, Usma, Gartner, Silvia, Blitz Castro, Enrique, Sole Jover, Amparo, Cox, Desmond, McKone, Edward, Plant, Barry, Williamson, Michael, Elnazir, Basil, Barbosa, Telma, Cols Roig, Maria, Burr, Lucy, Henderson, Daniel, Middleton, Peter, Kotsimbos, Tom, De Monestrol, Isabelle, Gilljam, Marita, Lindberg, Ulrika, Schwarz, Carsten, Bode, Sebastian, Epton, Michael, Halasz, Adrien, Laki, Istvan, O'Carroll, Mark, Fortner, Christopher, Bilodeau, Lara, Lapey, Allen, Moffett, Kathryn, Jia, Shijing, Uluer, Ahmet, Sears, Edmund, Keating, Claire, Omlor, Gregory, Mehdi, Nighat, Tupayachi Ortiz, Maria Gabriela, Messore, Barbara, Lambert, Allison, Mukadam, Zubin, Egan, Marie, Wilhelm, Andrew, Reyes, Santiago, Schaeffer, David, Szepfalusi, Zsolt, Epaud, Ralph, Leroy, Sylvie, Fischer Biner, Reta, Moeller, Alexander, Salvatore, Donatello, Johnson, Larry, Gohy, Sophie, Gramegna, Andrea, Olesen, Hanne, Tissot, Adrien, Marguet, Christophe, Desai, Maya, Owens, Louisa, Kherani, Tamizan, Sands, Dorota, Bakkeheim, Egil, Tullis, Elizabeth, Chilvers, Mark, Quon, Bradley, Lands, Larry, Parkins, Michael, Tremblay, Francois, Maitra, Anirban, Staples, Heather, Elidemir, Okan, Chatziagorou, Elpis, Tirakitsoontorn, Pornchai, Grenet, Dominique, Linnane, Barry, Nicholson, John Michael, Manika, Katerina, Tatopoulos, Aurelie, Pressler, Tacjana, Bagheri-Potthoff, Azadeh, Legg, Julian, Horsley, Alexander, Lee, Timothy, Houdouin, Veronique, Ramel, Sophie, Fajac, Isabelle, Sermet-Gaudelus, Isabelle, Kamphuis, Lieke, van der Ent, Kors, Vermeulen, Francois, Chiron, Raphael, Reix, Philippe, Van Braeckel, Eva, Knoop, Christiane, Vanderhelst, Eef, Durieu, Isabelle, Bui, Stephanie, Weiss, Laurence, Le Rouzic, Olivier, van der Meer, Renske, Roukema, Jolt, Altenburg, Josje, Robinson, Philip, Wainwright, Claire, Mulrennan, Siobhain, Clements, Barry, Taccetti, Giovanni, Cipolli, Marco, Dacco, Valeria, Fabrizzi, Benedetta, Castellani, Carlo, Eber, Ernst, Appelt, Dorothea, Studnicka, Michael, Sapiejka, Ewa, Mazurek, Henryk, Engan, Mette, Sauty, Alain, Mankikian, Julie, Yonker, Lael M ^b, Vermeulen, François ^c, Linnemann, Rachel W ^e, Braun, Andrew T ⁱ, Ramsey, Bonnie ^l, Mall, Marcus A ^{m, n, o}, Taylor-Cousar, Jennifer L ^p, McKone, Edward F ^q, Floreth, Tim ^s, Michelson, Peter ^s, Sosnay, Patrick R ^s, Nair, Nitin ^s, Zahigian, Rachel ^s, Martin, Hannah ^s, Ahluwalia, Neil ^s, Lam, Anna ^s

Source: In The Lancet Respiratory Medicine March 2025 13(3):256-271

Les évolutions thérapeutiques dans la prise en charge de la mucoviscidose

Alternate Title: Therapeutic developments in the management of cystic fibrosis (English)

Authors: Durieu, Isabelle ^{a, b, *, c}, Reynaud, Quitterie ^{a, b, c}

Source: In Sages-Femmes March-April 2025 24(2):8-10

Identification of carbapenemase-producing Enterobacteriaceae reservoirs in wet hospital environments as a potential factor in patient acquisition: A cross-sectional study in a French university hospital in 2023

Authors: Sleiman, Léna, Dananché, Cédric, Gardes, Sophie, Fredenucci, Isabelle, Duval, Camille, Durieu, Isabelle, Zoulim, Fabien, Vanhems, Philippe, Cassier, Pierre, Elias, Christelle

Source: In Infectious Diseases Now December 2024 54(8)

The expanded French compassionate programme for elexacaftor–tezacaftor–ivacaftor use in people with cystic fibrosis without a F508del CFTR variant: a real-world study

Authors: Kanaan, Reem, Carlier, Nicolas, Honoré, Isabelle, Chedevergne, Frédérique, Dreano, Elise, Hatton, Aurélie, Hinzpeter, Alexandre, Pranke, Iwona, Le Clainche-Viala, Laurence, Mayer, Sophie, Corvol, Harriet, Thouvenin, Guillaume, de Miranda, Sandra, Remus, Natascha, Douvry, Benoit, Duthoit, Louise, Perez, Thierry, Le Rouzic, Olivier, Wizla, Nathalie, Bon, Claire, Bui, Stéphanie, Poey, Nora, Stremler, Nathalie, Coltey, Bérengère, Dufeu, Nadine, Lebihan, Jean, Gabsi, Asma, Pouradier, Delphine, Andrejak, Claire, Rames, Cinthia, Dupuy-Grasset, Magali, Languepin, Jeanne, Marguet, Christophe, Pramil, Stéphanie, Arnouat, Baptiste, Fanton, Annlyse, Abely, Michel, Ravoninjatovo, Bruno, Blondé, Aurore, Guillaumot, Anne, Kieffer, Sebastien, Tatopoulos, Aurélie, Nove-Josserand, Raphaële, Ohlmann, Camille, Perrin, Thomas, Reynaud, Quitterie, Llerena, Catherine, Quétant, Sébastien, Valois, Sophie, Dalphin, Marie-Laure, Richaud-Thiriez, Bénédicte, Deneuville, Eric, Chiron, Raphael, Socchi, Floriane, Bihouée, Tiphaine, Mankikian, Julie, Flament, Thomas, Coolen-Allou, Nathalie, Gachelin, Elsa, Périsson, Caroline, Vuillard, Constance, Dupuis, Marion, Alkoussa, Wael, Marchal, Sarah, Leroy, Sylvie, Scalbert, Manuela, Campbell, Karine, Laurans, Muriel, Labbé, Guillaume, Montcouquiol, Sylvie, Priou, Pascaline, de Carli, Paola, Lemonnier, Lydie, Dehillotte, Clémence, Nouvel, Thierry, Burgel, Pierre-Régis ^*, Sermet-Gaudelus, Isabelle, Girodon, Emmanuelle, Durieu, Isabelle, Houdouin, Véronique, Audousset, Camille, Macey, Julie, Grenet, Dominique, Porzio, Michele, Murris-Espin, Marlène, Reix, Philippe, Baravalle, Mélisande, Belleguic, Chantal, Mely, Laurent, Verhille, Juliette, Weiss, Laurence, Reynaud-Gaubert, Martine, Mittaine, Marie, Hamidfar, Rebecca, Ramel, Sophie, Cosson, Laure, Danner-Boucher, Isabelle, Foucaud, Pierre, Roy, Charlotte, Burnet, Espérie, Raynal, Caroline, Audrezet, Marie-Pierre, Da Silva, Jennifer, Martin, Clémence

Source: In The Lancet Respiratory Medicine November 2024 12(11):888-900

Impact of COVID-19 infection on lung function and nutritional status amongst individuals with cystic fibrosis: A global cohort study

Authors: Kasmi, Irena, Drali, Ouardia, Burghart, Sabine, Lakatos-Krepcik, Andrea, Eder, Johannes, Jaksch, Peter, Kainz, Katharina, Kallinger, Margit, Leitner, Alexander, Mozdzen, Marta, Pfleger, Andreas, Renner, Sabine, Stadlinger, Martin, Thir, Christina, Nuriyev, Emil, Boboli, Hedwige, De Wachter, Elke, Dupont, Lieven, Gohy, Sophie, Hanssens, Laurence, Knoop, Christiane, Lammertyn, Elise, Nowé, Vicky, Pirson, Jessica, Thimmesch, Matthieu, Van Braeckel, Eva, Van Hoorenbeeck, Kim, Vanderhelst, Eef, Filho, Eduardo Piacentini, Athanazio, Rodrigo Abensur, Martins, Valéria de Carvalho, Duarte, Marta Cristina, Monte, Luciana de Freitas Velloso, de Fuccio, Marcelo Bicalho, Knabben, Adriana de Siqueira Carvalho, Melloti, Roberta, Meneses, Daniela Gois, Petrova, Guergana, Tješić-Drinković, Duška, Dugac, Andrea Vukić, Bambir, Ivan, Yiallouros, Panayiotis, Bilkova, Alena, Drevinek, Pavel, Macek, Milan, Jr, Olesen, Hanne Vebert, Pressler, Tania, Fouda, Eman Mahmoud, Nasr, Samya, Weldetsadik, Abate Yeshidinber, Al-iede, Montaha, Abdrakhmanov, Olzhas, Corvol, Harriet, Lemonnier-Videau, Lydie, Abely, Michel, Piccini, Carole Bailly, Belleguic, Chantal, Bihouee, Tiphaine, Billon, Yves, Bui, Stéphanie, Camara, Boubou, Cheraud, Marie-Christine, Chiron, Raphael, Duet, Emmanuelle Coirier, Cosson, Laure, Dalphin, Marie-Laure, Boucher, Isabelle Danner, De Miranda, Sandra, Deneuville, Eric, Dubus, Jean-Christophe, Durieu, Isabelle, Epaud, Ralph, Gerardin, Michèle, Grenet, Dominique, Houdouin, Véronique, Huet, Frédéric, Reem, Kanaan, Kessler, Romain, Languepin, Jeanne, Laurans, Muriel, Leroy, Sylvie, Llerena, Cathie, Macey, Julie, Mankikian, Julie, Marguet, Christophe, Martin, Clémence, Mely, Laurent, Mittaine, Marie, Murris-Espin, Marlène, Perisson, Caroline, Prevotat, Anne, Ramel, Sophie, Rames, Cinthia, Reix, Philippe, Revillon, Marine, Reynaud-Gaubert, Martine, Richaud-Thiriez, Bénédicte, Rittie, Jean-Luc, Scalbert-Dujardin, Manuëla, Sermet-Gaudelus, Isabelle, Storni, Véronique, Tatopoulos, Aurélie, Thouvenin, Guillaume, Troussier, Françoise, Weiss, Laurence, Wizla, Nathalie, Behl, Eva-Susanne, Brinkmann, Folke, Claßen, Martin, Graepler-Mainka, Ute, Griese, Matthias, Grübl, Armin, Hammermann, Jutta, Hebestreit, Helge, Heinzmann, Andrea, Herz, Alexander, Kiefer, Alexander, Kinder, Birte, Köster, Holger, Kuhnert, Stefan, Mainz, Jochen, Mayer, Angelika, Naehrig, Susanne, Niehues, Tim, Nüßlein, Thomas, Poplawska, Krystyna, Ringshausen, Felix, Rose, Markus, Rosenecker, Josef, Ruppel, Renate, Scharschinger, Anette, Schropp, Christian, Schwarz, Carsten, Smaczny, Christina, Sommerburg, Olaf, Sutharsan, Sivagurunathan, Stolz, Simone, Thomas, Wolfgang, Wege, Sabine, Welzenbach, Britta, Wollschläger, Bettina, Diamantea, Filia, Hatziagorou, Elpis, Manika, Katerina, Cox, Des, Elnazir, Basil, Fletcher, Godfrey, Gunaratnam, Cedric, McKone, Edward F., Plant, Barry J., Cohen-Cymberknoh, Malena, Gur, Michal, Livnat, Galit, Mei-Zahav, Meir, Amato, Annalisa, Ferrari, Gianluca, Badolato, Raffaele, Poli, Piercarlo, Battistini, Fiorella, Donati, Valentina, Bignamini, Elisabetta, Folino, Anna, Carnovale, Vincenzo, Castellani, Carlo, Casciaro, Rosaria, Cimino, Giuseppe, Cipolli, Marco, Lucca, Francesca, Collura, Mirella, Ficili, Francesca, Daccò, Valeria, Gagliano, Vanessa, Pizzamiglio, Giovanna, Mencarini, Valeria, Palladino, Nicola, Leonardi, Salvatore, Rotolo, Novella, Lucanto, Maria Cristina, Quattromano, Ester, Lucidi, Vincenzina, Majo, Fabio, Alghisi, Federico, Ciciriello, Fabiana, Manca, Antonio, Leonetti, Giuseppina, Maschio, Massimo, Messore, Barbara, Pantano, Stefano, Pisi, Giovanna, Spaggiari, Cinzia, Raia, Valeria, Laezza, Caterina, Ros, Mirco, Salvatore, Donatello, Taccetti, Giovanni, Francalanci, Michela, Vitullo, Pamela, Zolin, Anna, Aleksejeva, Elina, Malakauskas, Kestutis, Misevičiene, Valdone, Charatsi, Anna-Maria, la Barrière, Hélène De, Altenburg, Josje, Bannier, Michiel, Heijerman, Harry, Janssens, Hettie, Koppelman, Gerard, van der Meer, Renske, Merkus, Peter, Nuijsink, Marianne, Terheggen, Suzanne, van der Vaart, Hester, Wesseling, Geert-Jan, de Winter, Karin, Danevska, Ivana Arnaudova, Maretti, Tatjana Jakovska, Fustik, Stojka, Dziecichowicz-Latała, Daria, Wojsyk-Banaszak, Irena, Wozniacki, Lukasz, Amorim, Adelina, Santos, Ana Sofia Araújo, Castanhinha, Susana, Gamboa, Fernanda, Silva, Teresa Reis, Gonçalves, Fabienne, Pereira, Luísa, Ciuca, Ioana, Silva, Sónia, Csilla-Enikö, Szabo, Stan, Iustina, Amelina, Elena, Boitсova, Evgeniya, Chernyavskaya, Anastasia, Gorinova, Yuliya, Krasovskiy, Stanislav, Mukhina, Maria, Sherman, Victoria, Simonova, Olga, Kondratyeva, Elena, Bérešová, Eva, Bližnáková, Nina, Kayserová, Hana, Salobir, Barbara, Šelb, Julij, Krivec, Uroš, Fernandez, Antonio José Aguilar, Fernàndez, Antonio Alvarez, García, Félix Baranda, Aparicio, Marina Blanco, Corullón, Silvia Castillo, Cortell-Aznar, Isidoro, Pérez, Inés, Colomer, Jordi Costa i, Roig, María Cols, Pecellín, Isabel Delgado, Cáceres, Layla Diab, Paredes, Carmen Luna, Gartner, Silvia, Martínez, José Ramón Gutiérrez, Labarga, Inés Herrero, Girón-Moreno, Rosa Maria, Nogueira, Esperanza Jiménez, Ferreiro, Adelaida Lamas, Neyra, Alejandro López, Castro, Enrique Blitz, Galarraga, Laura Moreno, de Vincente, Carlos Martin, Navarro, Silvia Merlos, Nieto-Royo, Rosa, Fuster, Casilda Olveira, Pastor, Maria Dolores, Pérez-Ruiz, Estela, Prados-Sánchez, Concepción, Cancelo, Isabel Ramos, de Valbuena, Marta Ruiz, Asensi, José R. Villa, Santiago, Veronica Sanz, García, Patricia Fernández, Tawfeeq, Reem Mustafa, Banki, Adrienn, Gilljam, Marita, Krantz, Christina, Lindberg, Ulrika, Lindblad, Anders, Clarenbach, Christian, Steinack, Carolin, Hage, René, Schuurmans, Macé, Fischer, Reta, Kusche, Rachel, Rochat, Isabelle, Walter, Anna-Lena, Kamalaporn, Harutai, Hamouda, Samia, Tural, Dilber Ademhan, Ozcelik, Ugur, Asfuroğlu, Pelin, Eyüboğlu, Tuğba Şişmanlar, Aslan, Ayse Tana, Bingöl, Ayşen, Çobanoğlu, Nazan, Ozcan, Gizem, Dogru, Deniz, Gökdemir, Yasemin, KÖSE, Mehmet, Pekcan, Sevgi, Cosgriff, Rebecca, Semenchuk, Julie, Naito, Yumi, Charman, Susan C., Carr, Siobhán B, Cheng, Stephanie Y., Marshall, Bruce C., Faro, Albert, Elbert, Alexander, Gutierrez, Hector H., Goss, Christopher H., Karadag, Bulent, Burgel, Pierre-Régis, Colombo, Carla, Salvatore, Marco, Padoan, Rita, Daneau, Géraldine, Harutyunyan, Satenik, Kashirskaya, Nataliya, Kirwan, Laura, Middleton, Peter G, Ruseckaite, Rasa, de Monestrol, Isabelle, Naehrlich, Lutz, Mondejar-Lopez, Pedro, Jung, Andreas, van Rens, Jacqui, Bakkeheim, Egil, Orenti, Annalisa, Zomer-van Ommen, Domenique, da Silva-Filho, Luiz Vicente RF, Fernandes, Flavia Fonseca, Zampoli, Marco, Stephenson, Anne L.

Source: In Journal of Cystic Fibrosis September 2024 23(5):815-822

Health care resource utilization preceding death or lung transplantation in people with cystic fibrosis: HCRU before transplant or death in cystic fibrosis

Authors: Guyot, Erika, Reynaud, Quitterie, Belhassen, Manon, Bérard, Marjorie, Dehillotte, Clémence, Lemonnier, Lydie, Viprey, Marie, Van Ganse, Eric, Burgel, Pierre-Régis, Durieu, Isabelle

Source: In Journal of Cystic Fibrosis September 2024 23(5):903-909

Standards for the care of people with cystic fibrosis (CF); recognising and addressing CF health issues

Authors: Burgel, Pierre-Régis, Southern, Kevin W, Addy, Charlotte, Battezzati, Alberto, Berry, Claire, Bouchara, Jean-Philippe, Brokaar, Edwin, Brown, Whitney, Azevedo, Pilar, Durieu, Isabelle, Ekkelenkamp, Miquel, Finlayson, Felicity, Forton, Julian, Gardecki, Johanna, Hodkova, Pavla, Hong, Gina, Lowdon, Jacqueline, Madge, Su, Martin, Clémence, McKone, Edward, Munck, Anne, Ooi, Chee Y, Perrem, Lucy, Piper, Amanda, Prayle, Andrew, Ratjen, Felix, Rosenfeld, Margaret, Sanders, Don B, Schwarz, Carsten, Taccetti, Giovanni, Wainwright, Claire, West, Natalie E, Wilschanski, Michael, Bevan, Amanda, Castellani, Carlo, Drevinek, Pavel, Gartner, Silvia, Gramegna, Andrea, Lammertyn, Elise, Landau, Eddie (Edwina) C, Plant, Barry J, Smyth, Alan R, van Koningsbruggen-Rietschel, Silke, Middleton, Peter G.

Source: In Journal of Cystic Fibrosis March 2024 23(2):187-202

Monitoring of ECFS quality standards for the clinical management of adults with cystic fibrosis

Authors: Gramegna, Andrea, Aliberti, Stefano, Amorim, Adelina, Blasi, Francesco, Bourke, Stephen, Burgel, Pierre-Régis, Diamantea, Filia, Durieu, Isabelle, Fila, Libor, Moreno, Rosa María Girón, Messore, Barbara, Pokojová, Eva, Taccetti, Giovanni, Verhulst, Stijn, Dugac, Andrea Vukić, Wege, Sabine, Duff, Alistair, Southern, Kevin W., Castellani, Carlo

Source: In Journal of Cystic Fibrosis March 2024 23(2):306-313

Pathophysiologic implications of elevated prevalence of hereditary alpha-tryptasemia in all mastocytosis subtypes

Authors: Polivka, Laura, Madrange, Marine, Bulai-Livideanu, Cristina, Barete, Stéphane, Ballul, Thomas, Neuraz, Antoine, Greco, Celine, Agopian, Julie, Brenet, Fabienne, Dubreuil, Patrice, Burdet, Charles, Lemal, Richard, Tournilhac, Olivier, Terriou, Louis, Launay, David, Bouillet, Laurence, Gourguechon, Clément, Damaj, Ghandi, Frenzel, Laurent, Meni, Cécile, Bouktit, Hassiba, Collange, Anne Florence, Gaudy-Marqueste, Caroline, Gousseff, Marie, Le Mouel, Edwige, Hamidou, Mohamed, Neel, Antoine, Ranta, Dana, Jaussaud, Roland, Guilpain, Philippe, Canioni, Danielle, Molina, Thierry Jo, Bruneau, Julie, Lhermitte, Ludovic, Garcelon, Nicolas, Javier, Rose-Marie, Pelletier, Fabien, Castelain, Florence, Retornaz, Frederique, Cabrera, Quentin, Zunic, Patricia, Gourin, Marie Pierre, Wierzbicka-Hainaut, Ewa, Viallard, Jean François, Lavigne, Christian, Hoarau, Cyrille, Durieu, Isabelle, Heiblig, Maël, Dimicoli-Salazar, Sophie, Torregrosa-Diaz, Jose Miguel, Soria, Angèle, Arock, Michel, Lortholary, Olivier, Bodemer, Christine, Hermine, Olivier, Rossignol, Julien

Source: In The Journal of Allergy and Clinical Immunology January 2024 153(1):349-353

Nonsense mutations accelerate lung disease and decrease survival of cystic fibrosis children

Authors: Orenti, Annalisa ^*, Pranke, Iwona ^*, Faucon, Caroline, Varilh, Jessica, Hatton, Aurelie, Golec, Anita, Dehillotte, Clemence, Durieu, Isabelle, Reix, Philippe, Burgel, Pierre-Régis, Grenet, Dominique, Tasset, Céline, Gachelin, Elsa, Perisson, Caroline, Lepissier, Agathe, Dreano, Elise, Tondelier, Danielle, Chevalier, Benoit, Weiss, Laurence, Kiefer, Sébastien, Laurans, Muriel, Chiron, Raphael, Lemonnier, Lydie, Marguet, Christophe, Jung, Andreas, Edelman, Aleksander, Kerem, Bat-Sheva, Girodon, Emmanuelle, Taulan-Cadars, Magali, Hinzpeter, Alexandre, Kerem, Eitan, Naehrlich, Lutz, Sermet-Gaudelus, Isabelle

Source: In Journal of Cystic Fibrosis November 2023 22(6):1070-1079

Pregnancy outcomes in women with primary Sjögren's syndrome: an analysis of data from the multicentre, prospective, GR2 study

Authors: AUDEMARD-VERGER, Alexandra, AZZI, Emmanuel, BANNEVILLE, Béatrice, BAUDET, Antoine, BEAUDOUIN BAZIRE, Constance, BELIZNA, Cristina, Belot, Alexandre, BENHAMOU, Ygal, Berezné, Alice, BERNARD-GUERVILLY, Fanny, BERTHIER, Sabine, BEZANAHARY, Holy, BIALE, Lisa, BIGOT, Adrien, BLANCHARD-DELAUNAY, Claire, CALAS, Anne, CAMPAGNE, Julien, CATHEBRAS, Pascal, CAZALETS, Claire, CHAIGNE, Benjamin, CHANDESRIS, Olivia, CHATELAIS, Jérémy, CHATELUS, Emmanuel, COHEN, Fleur, Combe, Bernard, COMPARON, Céline, COQUERELLE, Pascal, DAMIAN, Louise, DAUGAS, Eric, DE MENTHON, Mathilde, DE MOREUIL, Claire, DELATTRE, Estelle, DELLAL, Azeddine, Deneux-Tharaux, Catherine, DENIS, Amélie, DEPROUW, Camille, DERNIS, Emmanuelle, DEROUX, Alban, DESOUCHES, Sandra, Dieudé, Philippe, DIREZ, Guillaume, Dougados, Maxime, DRIESSEN, Marine, DU THANH, Aurélie, DUNOGEANT, Laetitia, DURANT, Cécile, DUREL, Cécile-Audrey, DURIEU, Isabelle, EBOUE, Florence, Elefant, Elisabeth, FAIN, Olivier, FAUTREL, Bruno, FLIPO, René-Marc, FRAZIER, Aline, FROISSART, Antoine, GEORGIN-LAVIALLE, Sophie, GERVAIS, Elisabeth, GODEAU, Bertrand, Goffinet, François, GOMPEL, Anne, GOSSEC, Laure, GOUPILLE, Philippe, GRANGE, Claire, GUILLAUD-DANIS, Constance, HACHULLA, Eric, HOEFSLOOT, Sabine, HUMMEL, Aurélie, JEGO, Patrick, JOBARD, Stéphanie, JOSSELIN-MAHR, Laurence, LAMBERT, Marc, LANGLOIS, Vincent, LARIVIERE, Delphine, LARROCHE, Claire, LATOURTE, Augustin, LAVIGNE, Christian, LE GALLOU, Thomas, LEROUX, Gaëlle, LETAROUILLY, Jean Guillaume, LIOTÉ, Frédéric, Loeuillet, Laurence, London, Jonathan, Loustau, Valentine, LOZAC'H, Pierre, MAHEU, Emmanuel, MAILLARD, Hélène, MAROTTE, Hubert, MASSEAU, Agathe, MEKINIAN, Arsène, Melboucy Belkhir, Sara, Miceli-Richard, Corinne, MICHAUD, Martin, MICHEL, Marc, MORANNE, Olivier, MORATI-HAFSAOUI, Chafika, MOULIS, Guillaume, MOUTHON, Luc, NICOLAS, Barbara, Nizard, Jacky, ORA, Jérémy, OUTH, Rodérau, PASQUIER, Elisabeth, PENNAFORTE, Jean-Loup, PERLAT, Antoinette, PETIT-BAUER, Hélène, PILLEBOUT, Evangeline, PIOT, Jean-Maxime, PORTIER, Agnès, Pourrat, Olivier, PUECHAL, Xavier, PUGNET, Gregory, REDONDIN, Manon, REGENT, Alexis, RORIZ, Mélanie, SAILLER, Laurent, SAVEY, Léa, SCHERLINGER, Marc, SCHLEINITZ, Nicolas, Sellam, Jérémie, Sentilhes, Loïc, SERVAIS, Aude, SMETS, Perrine, SORDET, Christelle, SOUBRIER, Martin, STANKOVIC-STOJANOVIC, Katia, URBANSKI, Geoffrey, VEIT, Véronique, WEBER, Emmanuelle, YELNIK, Cécile, de Frémont, Grégoire Martin, Costedoat-Chalumeau, Nathalie, Lazaro, Estibaliz, Belkhir, Rakiba, Guettrot-Imbert, Gaëlle, Morel, Nathalie, Nocturne, Gaétane, Molto, Anna, Goulenok, Tiphaine, Diot, Elisabeth, Perard, Laurent, Ferreira-Maldent, Nicole, Le Besnerais, Maelle, Limal, Nicolas, Martis, Nihal, Abisror, Noémie, Debouverie, Odile, Richez, Christophe, Sobanski, Vincent, Maurier, François, Sauvetre, Gaëtan, Levesque, Hervé, Timsit, Marie-Agnès, Tieulié, Nathalie, Orquevaux, Pauline, Bienvenu, Boris, Mahevas, Matthieu, Papo, Thomas, Lartigau-Roussin, Céline, Chauvet, Elodie, Berthoux, Emilie, Sarrot-Reynauld, Françoise, Raffray, Loïc, Couderc, Marion, Silva, Nicolas Martin, Jourde-Chiche, Noémie, Belhomme, Nicolas, Thomas, Thierry, Poindron, Vincent, Queyrel-Moranne, Viviane, Delforge, Juliette, Le Ray, Camille, Pannier, Emmanuelle, Mariette, Xavier, Le Guern, Véronique ^*, Seror, Raphaèle ^{*, *}

Source: In The Lancet Rheumatology June 2023 5(6):e330-e340

Allogeneic stem cell transplantation compared to conservative management in adults with inborn errors of immunity

Authors: Cheminant, Morgane, Fox, Thomas A., Alligon, Mickael, Bouaziz, Olivier, Neven, Bénédicte, Moshous, Despina, Blanche, Stéphane, Guffroy, Aurélien, Fieschi, Claire, Malphettes, Marion, Schleinitz, Nicolas, Perlat, Antoinette, Viallard, Jean-François, Dhedin, Nathalie, Sarrot-Reynauld, Françoise, Durieu, Isabelle, Humbert, Sébastien, Fouyssac, Fanny, Barlogis, Vincent, Carpenter, Benjamin, Hough, Rachael, Laurence, Arian, Marçais, Ambroise, Chakraverty, Ronjon, Hermine, Olivier, Fischer, Alain, Burns, Siobhan O., Mahlaoui, Nizar, Morris, Emma C. ^∗, Suarez, Felipe ^{∗, ∗}

Source: In Blood 5 January 2023 141(1):60-71

Characterisation of a high-risk profile for maternal thrombotic and severe haemorrhagic complications in pregnant women with antiphospholipid syndrome in France (GR2): a multicentre, prospective, observational study

Authors: Azzi, Emmanuel, Banneville, Béatrice, Baudet, Antoine, Beaudouin-Bazire, Constance, Belizna, Cristina, Belkhir, Rakiba, Berezne, Alice, Berthoux, Emilie, Berthier, Sabine, Biale, Lisa, Bienvenu, Boris, Blanchard-Delaunay, Claire, Cathebras, Pascal, Cazalets, Claire, Chaigne, Benjamin, Chandesris, Olivia, Chatelais, Jérémy, Chatelus, Emmanuel, Coquerelle, Pascal, Couderc, Marion, Delforge, Juliette, Denis, Amélie, Desouches, Sandra, Dieudé, Philippe, Direz, Guillaume, Driessen, Marine, Du Thanh, Aurélie, Dunogeant, Laetitia, Durant, Cécile, Durieu, Isabelle, Fabre, Marc, Fain, Olivier, Flipo, René-Marc, Frazier, Aline, Froissart, Antoine, Georgin-Lavialle, Sophie, Gervais, Elisabeth, Gompel, Anne, Gossec, Laure, Goupille, Phillipe, Grange, Claire, Guillaud-Danis, Constance, Hummel, Aurélie, Jallouli, Moez, Jego, Patrick, Jobard, Stéphane, Josselin-Mahr, Laurence, Jourde-Chiche, Noémie, Korganow, Anne-Sophie, Lambert, Marc, Lariviere, Delphine, Larroche, Claire, Lartigau-Roussin, Céline, Latourte, Augustin, Le Gallou, Thomas, Leroux, Gaëlle, Levesque, Hervé, Lioté, Frédéric, London, Jonathan, Loustau, Valentine, Maheu, Emmanuel, Mahevas, Matthieu, Maillard, Hélène, Mariette, Xavier, Marotte, Hubert, Martin-Silva, Nicolas, Martis, Nihal, Masseau, Agathe, Mekinian, Arsène, Melboucy-Belkhir, Sara, Michaud, Martin, Michel, Marc, Morati-Hafsaoui, Chafika, Nizard, Jacky, Ora, Jérémy, Pennaforte, Jean-Loup, Perlat, Antoinette, Petit Bauer, Hélène, Pillebout, Evangeline, Piot, Jean-Maxime, Portier, Agnès, Pugnet, Gregory, Redondin, Manon, Regent, Alexis, Richez, Christophe, Roriz, Mélanie, Sailler, Laurent, Sauvêtre, Gaëtan, Savey, Léa, Sobanski, Vincent, Sordet, Christelle, Soubrier, Martin, Stankovic Stojanovic, Katia, Thomas, Thierry, Timsit, Marie-Agnès, Tsatsaris, Vassilis, Murarasu, Anne, Guettrot-Imbert, Gaëlle, Le Guern, Véronique, Yelnik, Cécile, Queyrel, Viviane, Schleinitz, Nicolas, Ferreira-Maldent, Nicole, Diot, Elisabeth, Urbanski, Geoffrey, Pannier, Emmanuelle, Lazaro, Estibaliz, Souchaud-Debouverie, Odile, Orquevaux, Pauline, Belhomme, Nicolas, Morel, Nathalie, Chauvet, Elodie, Maurier, François, Le Besnerais, Maëlle, Abisror, Noemie, Goulenok, Tiphaine, Sarrot-Reynauld, Françoise, Deroux, Alban, Pasquier, Elisabeth, de Moreuil, Claire, Bezanahary, Holy, Pérard, Laurent, Limal, Nicolas, Langlois, Vincent, Calas, Anne, Godeau, Bertrand, Lavigne, Christian, Hachulla, Eric, Cohen, Fleur, Benhamou, Ygal, Raffray, Loïc, de Menthon, Mathilde, Tieulié, Nathalie, Poindron, Vincent, Mouthon, Luc, Larosa, Maddalena, Eléfant, Elisabeth, Sentilhes, Loic, Molto, Anna, Deneux-Tharaux, Catherine, Costedoat-Chalumeau, Nathalie ^*

Source: In The Lancet Rheumatology December 2022 4(12):e842-e852

Serological response to SARS-CoV-2 vaccination in patients with inflammatory rheumatic disease treated with disease modifying anti-rheumatic drugs: A cohort study and a meta-analysis

Authors: Auroux, Maxime, Laurent, Benjamin, Coste, Baptiste, Massy, Emmanuel, Mercier, Alexandre, Durieu, Isabelle, Confavreux, Cyrille B., Lega, Jean-Christophe, Mainbourg, Sabine, Coury, Fabienne

Source: In Joint Bone Spine October 2022 89(5)

Réponse sérologique après vaccination contre le coronavirus chez les patients atteints de rhumatisme inflammatoire chronique traités par DMARDs : étude de cohorte et revue systématique avec méta-analyse

Authors: Auroux, Maxime, Laurent, Benjamin, Coste, Baptiste, Massy, Emmanuel, Mercier, Alexandre, Durieu, Isabelle, Confavreux, Cyrille B, Lega, Jean-Christophe, Mainbourg, Sabine, Coury, Fabienne

Source: In Revue du rhumatisme October 2022 89(5):435-446

Indirect Comparison of Glucocorticoid-Sparing Agents for Remission Maintenance in Giant Cell Arteritis: A Network Meta-analysis

Authors: Mainbourg, Sabine, Tabary, Axel, Cucherat, Michel, Gueyffier, François, Lobbes, Hervé, Aussedat, Marie, Grenet, Guillaume, Durieu, Isabelle, Samson, Maxime, Lega, Jean Christophe

Source: In Mayo Clinic Proceedings October 2022 97(10):1824-1835

An appraisal of the frequency and severity of noninfectious manifestations in primary immunodeficiencies: A study of a national retrospective cohort of 1375 patients over 10 years

Authors: Abou-Chahla, Wadih, Adoue, Daniel, Aladjidi, Nathalie, Armari-Alla, Corinne, Barlogis, Vincent, Bayart, Sophie, Bertrand, Yves, Blanche, Stéphane, Bodet, Damien, Bonnotte, Bernard, Borie, Raphaël, Boutard, Patrick, Boutboul, David, Briandet, Claire, Brion, Jean-Paul, Brouard, Jacques, Carausu, Liana, Castelle, Martin, Cathebras, Pascal, Catherinot, Emilie, Cheikh, Nathalie, Cheminant, Morgane, Cohen-Beaussant, Sarah, Comont, Thibault, Couderc, Louis-Jean, Cougoul, Pierre, Couillault, Gérard, Crevon, Lionel, Demonchy, Elisa, Deville, Anne, Devoldere, Catherine, Dore, Eric, Dulieu, Fabienne, Durieu, Isabelle, Entz-Werle, Natacha, Fieschi, Claire, Fouyssac, Fanny, Frange, Pierre, Gajdos, Vincent, Galicier, Lionel, Gandemer, Virginie, Gardembas, Martine, Gaud, Catherine, Grosbois, Bernard, Guffroy, Aurélien, Guitton, Corinne, Guillerm, Gaëlle, Hachulla, Eric, Hamidou, Mohamed, Haro, Sophie, Hatchuel, Yves, Hermine, Olivier, Hoarau, Cyrille, Hot, Arnaud, Humbert, Sébastien, Jaccard, Arnaud, Jais, Jean-Philippe, Jannier, Sarah, Jacquot, Serge, Jaussaud, Roland, Jeandel, Pierre-Yves, Jeziorski, Eric, Kebaili, Kamila, Korganow, Anne-Sophie, Lambotte, Olivier, Lanternier, Fanny, Larroche, Claire, Launay, David, Le Moigne, Emmanuelle, Le Quellec, Alain, Le Moing, Vincent, Lebranchu, Yvon, Lecuit, Marc, Lefèvre, Guillaume, Lelièvre, Jean-Daniel, Lemal, Richard, Li-Thiao-Te, Valérie, Lortholary, Olivier, Luca, Luminita, Mallebranche, Coralie, Malphettes, Marion, Marie-Cardine, Aude, Martin-Silva, Nicolas, Masseau, Agathe, Mazingue, Françoise, Merlin, Etienne, Michel, Gérard, Millot, Frédéric, Miot, Charline, Monlibert, Béatrice, Monpoux, Fabrice, Moshous, Despina, Mouthon, Luc, Münzer, Martine, Navarro, Robert, Neven, Bénédicte, Nouar, Dalila, Nove-Josserand, Raphaële, Oksenhendler, Eric, Ouachée-Chardin, Marie, Pagnier, Anne, Pasquet, Marlène, Pellier, Isabelle, Perel, Yves, Perlat, Antoinette, Piguet, Christophe, Plantaz, Dominique, Rivière, Sophie, Roblot, Pascal, Rohrlich, Pierre-Simon, Royer, Bruno, Salle, Valéry, Sarrot-Reynauld, Françoise, Servettaz, Amélie, Stephan, Jean-Louis, Schleinitz, Nicolas, Sokol, Harry, Suarez, Felipe, Swiader, Laure, Taque, Sophie, Thomas, Caroline, Tournilhac, Olivier, Thumerelle, Caroline, Vannier, Jean-Pierre, Viallard, Jean-François, Alligon, Mickaël, Mahlaoui, Nizar, Courteille, Virginie, Costes, Laurence, Afonso, Veronica, Randrianomenjanahary, Philippe, de Vergnes, Nathalie, Ranohavimparany, Anja, Vo, Duy, Hafsa, Inès, Bach, Perrine, Benoit, Vincent, Garcelon, Nicolas, Fischer, Alain

Source: In The Journal of Allergy and Clinical Immunology June 2022 149(6):2116-2125

Sustained effectiveness of elexacaftor-tezacaftor-ivacaftor in lung transplant candidates with cystic fibrosis

Authors: Martin, Clémence, Reynaud-Gaubert, Martine, Hamidfar, Rebecca, Durieu, Isabelle, Murris-Espin, Marlène, Danner-Boucher, Isabelle, Chiron, Raphaël, Leroy, Sylvie, Douvry, Benoit, Grenet, Dominique, Mely, Laurent, Ramel, Sophie, Montcouquiol, Sylvie, Lemonnier, Lydie, Burnet, Espérie, Paillasseur, Jean-Louis, Da Silva, Jennifer, Burgel, Pierre-Régis

Source: In Journal of Cystic Fibrosis May 2022 21(3):489-496

Safety and pharmacokinetics of Roscovitine (Seliciclib) in cystic fibrosis patients chronically infected with Pseudomonas aeruginosa, a randomized, placebo-controlled study

Authors: Meijer, Laurent, Hery-Arnaud, Geneviève, Leven, Cyril, Nowak, Emmanuel, Hillion, Sophie, Renaudineau, Yves, Durieu, Isabelle, Chiron, Raphaël, Prevotat, Anne, Fajac, Isabelle, Hubert, Dominique, Murris-Espin, Marlène, Huge, Sandrine, Danner-Boucher, Isabelle, Ravoninjatovo, Bruno, Leroy, Sylvie, Macey, Julie, Urban, Thierry, Rault, Gilles, Mottier, Dominique, Berre, Rozenn Le

Source: In Journal of Cystic Fibrosis May 2022 21(3):529-536

Prevalence of Post–Glucose Challenge Hypoglycemia in Adult Patients With Cystic Fibrosis and Relevance to the Risk of Cystic Fibrosis–Related Diabetes

Authors: Bonhoure, Anne, Potter, Kathryn J., Reynaud, Quitterie, Boudreau, Valérie, Senior, Peter A., Tremblay, François, Lavoie, Annick, Durieu, Isabelle, Rabasa-Lhoret, Rémi

Source: In Canadian Journal of Diabetes April 2022 46(3):294-301